Autoantibody stabilization of the classical pathway C3 convertase leading to C3 deficiency and Neisserial sepsis: C4 nephritic factor revisited

Clinical Immunology

Volumn 145, Issue 3, 2012, Pages 241-250

  Miller, Elizabeth C ^a   Chase, Nicole M ^b,d   Densen, Peter ^c   Hintermeyer, Mary K ^b   Casper, James T ^b   Atkinson, John P ^a  

^a WASHINGTON UNIVERSITY   (United States)

^b MEDICAL COLLEGE OF WISCONSIN   (United States)

^c UNIVERSITY OF IOWA   (United States)

^d Midwest Immunology Clinic   (United States)

Author keywords

Autoimmunity; C3 deficiency; C4 nephritic factor; Neisserial infection

Indexed keywords

ACICLOVIR; AUTOANTIBODY; C4 NEPHRITIC FACTOR; CEFTRIAXONE; CLASSICAL COMPLEMENT PATHWAY C3 C5 CONVERTASE; COMPLEMENT COMPONENT C1; COMPLEMENT COMPONENT C2; COMPLEMENT COMPONENT C3B; CORTICOSTEROID; CREATINE KINASE; CREATINE KINASE MB; IMMUNOGLOBULIN G ANTIBODY; MENINGOCOCCUS VACCINE; NEPHRITIC FACTOR; NORADRENALIN; PNEUMOCOCCUS VACCINE; TROPONIN; UNCLASSIFIED DRUG;

ABDOMINAL PAIN; ADULT; ANTIBIOTIC THERAPY; ANTIBODY TITER; ARTICLE; BLOOD CELL COUNT; BLOOD SAMPLING; BRAIN ISCHEMIA; CASE REPORT; COMPLEMENT C3 DEFICIENCY; COMPLEMENT DEFICIENCY; DISEASE SEVERITY; ECHOCARDIOGRAPHY; ENZYME LINKED IMMUNOSORBENT ASSAY; EXON; FEVER; FOLLOW UP; HEADACHE; HELICOBACTER INFECTION; HEMOLYSIS; HUMAN; HYPOTENSION; IMMUNIZATION; INTENSIVE CARE UNIT; INTRON; LEUKOCYTOSIS; LUMBAR PUNCTURE; MALE; MEDICAL HISTORY; MEMBRANOPROLIFERATIVE GLOMERULONEPHRITIS; MENINGOCOCCOSIS; MYOCARDITIS; NAUSEA AND VOMITING; NEISSERIA MENINGITIDIS; NEISSERIACEAE INFECTION; NUCLEAR MAGNETIC RESONANCE IMAGING; NUCLEOTIDE SEQUENCE; POLYACRYLAMIDE GEL ELECTROPHORESIS; PRIORITY JOURNAL; PROTEIN BLOOD LEVEL; PROTEIN DEGRADATION; PULMONARY HYPERTENSION; SEPSIS; SEQUENCE ANALYSIS; SEROTYPE; TACHYCARDIA; THROMBOCYTOPENIA; WESTERN BLOTTING;

ADOLESCENT; AUTOANTIBODIES; COMPLEMENT C3; COMPLEMENT C3 CONVERTASE, CLASSICAL PATHWAY; COMPLEMENT C5 CONVERTASE, CLASSICAL PATHWAY; COMPLEMENT SYSTEM PROTEINS; ENZYME STABILITY; HUMANS; IMMUNOGLOBULIN G; MALE; MENINGITIS, MENINGOCOCCAL; MENINGOCOCCAL INFECTIONS; MODELS, IMMUNOLOGICAL; SEPSIS; SEQUENCE ANALYSIS, DNA;

EID: 84867898001     PISSN: 15216616     EISSN: 15217035     Source Type: Journal    
DOI: 10.1016/j.clim.2012.09.007     Document Type: Article

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