Entorhinal cortical neurons are the primary targets of FUS mislocalization and ubiquitin aggregation in FUS transgenic rats

Human Molecular Genetics

Volumn 21, Issue 21, 2012, Pages 4602-4614

  Huang, Cao ^a   Tong, Jianbin ^a   Bi, Fangfang ^a   Wu, Qinxue ^a   Huang, Bo ^a   Zhou, Hongxia ^a   Xia, Xu Gang ^a  

^a THOMAS JEFFERSON UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

FUSED IN SARCOMA PROTEIN; MUTANT PROTEIN; ROSIGLITAZONE; TAR DNA BINDING PROTEIN; UBIQUITIN;

AMNESIA; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BRAIN CELL; CONTROLLED STUDY; DENDRITIC CELL; DENDRITIC SPINE; DISEASE MODEL; ENTORHINAL CORTEX; FRONTOTEMPORAL DEMENTIA; GENE MUTATION; GENE OVEREXPRESSION; GENETIC ASSOCIATION; GLIA; GOLGI COMPLEX; MITOCHONDRION; NERVE CELL CULTURE; NONHUMAN; PATHOLOGY; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN EXPRESSION; PROTEIN LOCALIZATION; RAT; SPATIAL MEMORY; TEMPORAL LOBE; TRANSGENE; TRANSGENIC RAT;

ANIMALS; DENDRITIC SPINES; DISEASE MODELS, ANIMAL; DNA-BINDING PROTEINS; ENTORHINAL CORTEX; FRONTOTEMPORAL LOBAR DEGENERATION; GENE EXPRESSION REGULATION; GOLGI APPARATUS; HUMANS; MEMORY DISORDERS; MITOCHONDRIA; MUTATION; PPAR GAMMA; PROSENCEPHALON; RATS; RATS, TRANSGENIC; RNA-BINDING PROTEIN FUS; THIAZOLIDINEDIONES; UBIQUITIN;

EID: 84867289496     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/dds299     Document Type: Article

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