A multinational, multidisciplinary consensus for the diagnosis and management of spinal cord compression among patients with mucopolysaccharidosis VI

Molecular Genetics and Metabolism

Volumn 107, Issue 1-2, 2012, Pages 15-24

  Solanki, Guirish A ^a   Alden, Tord D ^b   Burton, Barbara K ^b   Giugliani, Roberto ^c   Horovitz, Dafne D G ^d   Jones, Simon A ^e   Lampe, Christina ^f   Martin, Kenneth W ^g   Ryan, Maura E ^b   Schaefer, Matthias K ^h   Siddiqui, Aisha ^b   White, Klane K ⁱ   Harmatz, Paul ^g  

^a BIRMINGHAM CHILDREN S HOSPITAL   (United Kingdom)

^b CHILDREN'S MEMORIAL HOSPITAL   (United States)

^c HOSPITAL DE CLÍNICAS DE PORTO ALEGRE   (Brazil)

^d INSTITUTO OSWALDO CRUZ   (Brazil)

^e ST MARY S HOSPITAL   (United Kingdom)

^f UNIVERSITY MEDICAL CENTER MAINZ   (Germany)

^g CHILDREN S HOSPITAL OAKLAND   (United States)

^h Department of Anesthesiology Intensive Care Emergency Medicine and Pain Therapy   (Germany)

ⁱ SEATTLE CHILDREN S HOSPITAL   (United States)

Author keywords

Airway management; Cervical cord compression; Practice guideline; Spinal cord compression; Surgical decompression

Indexed keywords

ANESTHESIOLOGICAL PROCEDURE; CERVICAL CORD COMPRESSION; CLINICAL FEATURE; CLINICAL PRACTICE; COMPUTER ASSISTED TOMOGRAPHY; CONSENSUS DEVELOPMENT; ELECTROCARDIOGRAM; ENZYME REPLACEMENT; EVOKED RESPONSE; EXERCISE TEST; EXTUBATION; FUNCTIONAL ASSESSMENT; HEMATOPOIETIC STEM CELL TRANSPLANTATION; HUMAN; MAROTEAUX LAMY SYNDROME; NEUROLOGIC EXAMINATION; NEUROPHYSIOLOGY; NUCLEAR MAGNETIC RESONANCE IMAGING; PATIENT CARE; PATIENT MONITORING; POSITIVE END EXPIRATORY PRESSURE; PRACTICE GUIDELINE; PRIORITY JOURNAL; REVIEW; SPINAL CORD COMPRESSION; SPINAL CORD DECOMPRESSION; SPINAL CORD DISEASE; SPINAL CORD FUNCTION; SURGICAL TECHNIQUE;

CERVICAL VERTEBRAE; CONSENSUS DEVELOPMENT CONFERENCES AS TOPIC; HUMANS; MUCOPOLYSACCHARIDOSIS VI; PRACTICE GUIDELINES AS TOPIC; SPINAL CORD COMPRESSION;

EID: 84866165908     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2012.07.018     Document Type: Review

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