Clinical severity of Huntington's disease does not always correlate with neuropathologic stage

Movement Disorders

Volumn 27, Issue 9, 2012, Pages 1099-1103

  Pillai, Jagan A ^a   Hansen, Lawrence A ^b   Masliah, Eliezer ^b   Goldstein, Jody L ^b   Edland, Steven D ^b   Corey Bloom, Jody ^b,c  

^a LERNER RESEARCH INSTITUTE   (United States)

^b UNIVERSITY OF CALIFORNIA   (United States)

^c VA SAN DIEGO HEALTHCARE SYSTEM   (United States)

Author keywords

Autopsy study; Huntington's disease; Independence Scale; Total Functional Capacity; Unified Huntington's Disease Rating Scale; Vonsattel staging

Indexed keywords

ADULT; AGED; ARTICLE; AUTOPSY; BRAIN WEIGHT; CAG REPEAT; CLINICAL ARTICLE; CLINICAL ASSESSMENT TOOL; DISEASE COURSE; DISEASE SEVERITY; EDUCATIONAL STATUS; FEMALE; GENETIC ANALYSIS; HUMAN; HUNTINGTON CHOREA; MALE; MINI MENTAL STATE EXAMINATION; MORTALITY; ONSET AGE; PHENOTYPE; PRIORITY JOURNAL; RATING SCALE; SCORING SYSTEM; UNIFIED HUNTINGTON DISEASE RATING SCALE;

ADULT; AGE OF ONSET; AGED; AGED, 80 AND OVER; AUTOPSY; BRAIN; COGNITION DISORDERS; FEMALE; HUMANS; HUNTINGTON DISEASE; MALE; MIDDLE AGED; NEUROPSYCHOLOGICAL TESTS; ORGAN SIZE; PHENOTYPE;

EID: 84864775018     PISSN: 08853185     EISSN: 15318257     Source Type: Journal    
DOI: 10.1002/mds.25026     Document Type: Article

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