Outcomes of childhood pulmonary arterial hypertension in BMPR2 and ALK1 mutation carriers

American Journal of Cardiology

Volumn 110, Issue 4, 2012, Pages 586-593

  Chida, Ayako ^a,b   Shintani, Masaki ^b   Yagi, Hisato ^b   Fujiwara, Maya ^b,c   Kojima, Yasuko ^b,c   Sato, Hiroki ^a   Imamura, Shinichiro ^b,d   Yokozawa, Masato ^e   Onodera, Norio ^f   Horigome, Hitoshi ^g   Kobayashi, Tomio ^h   Hatai, Yoshiho ^a   Nakayama, Tomotaka ^c   Fukushima, Hiroyuki ⁱ   Nishiyama, Mitsunori ^j,k   Doi, Shouzaburo ^k   Ono, Yasuo ^l   Yasukouchi, Satoshi ^m   Ichida, Fukiko ⁿ   Fujimoto, Kazuto ^o   Ohtsuki, Shinichi ^p   Teshima, Hidetaka ^q   Kawano, Tatsuya ^r   Nomura, Yuichi ^s   Gu, Hong ^t   Ishiwata, Takahiro ^a   Furutani, Yoshiyuki ^b   Inai, Kei ^b   Saji, Tsutomu ^c   Matsuoka, Rumiko ^b,u   Nonoyama, Shigeaki ^a   Nakanishi, Toshio ^b   more..

^a NATIONAL DEFENSE MEDICAL COLLEGE   (Japan)

^b TOKYO WOMEN'S MEDICAL UNIVERSITY   (Japan)

^c TOHO UNIVERSITY OMORI MEDICAL CENTER   (Japan)

^d HIMEJI DOKKYO UNIVERSITY   (Japan)

^e HOKKAIDO MEDICAL CENTER   (Japan)

^f Iwate Prefectural Kitakami Hospital   (Japan)

^g UNIVERSITY OF TSUKUBA   (Japan)

^h Gumna Children S Medical Center   (Japan)

ⁱ KEIO UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^j Sakakibara Memorial Hospital   (Japan)

^k TOKYO MEDICAL AND DENTAL UNIVERSITY   (Japan)

^l SHIZUOKA CHILDREN'S HOSPITAL   (Japan)

^m NAGANO CHILDREN'S HOSPITAL   (Japan)

ⁿ UNIVERSITY OF TOYAMA   (Japan)

^o KYOTO SECOND RED CROSS HOSPITAL   (Japan)

^p OKAYAMA UNIVERSITY   (Japan)

^q NATIONAL HOSPITAL ORGANIZATION NAGASAKI MEDICAL CENTER   (Japan)

^r OITA UNIVERSITY   (Japan)

^s KAGOSHIMA UNIVERSITY   (Japan)

^t CAPITAL MEDICAL UNIVERSITY   (China)

^u TOHO UNIVERSITY   (Japan)

more..

Author keywords

[No Author keywords available]

Indexed keywords

ACTIVIN RECEPTOR LIKE KINASE 1; AMBRISENTAN; ANTICOAGULANT AGENT; BONE MORPHOGENETIC PROTEIN RECEPTOR 2; BOSENTAN; CARDIOTONIC AGENT; DIURETIC AGENT; OXYGEN; PROSTACYCLIN; SILDENAFIL; TADALAFIL; VASODILATOR AGENT;

ANTICOAGULANT THERAPY; ANTIHYPERTENSIVE THERAPY; ARTICLE; CHILDHOOD DISEASE; CHILDHOOD MORTALITY; CONTROLLED STUDY; DRUG RESPONSE; FEMALE; FRAMESHIFT MUTATION; FUNCTIONAL STATUS; GENE DELETION; GENE MUTATION; HETEROZYGOTE; HUMAN; LUNG TRANSPLANTATION; MAJOR CLINICAL STUDY; MALE; MISSENSE MUTATION; NONSENSE MUTATION; ONSET AGE; OUTCOME ASSESSMENT; OVERALL SURVIVAL; OXYGEN THERAPY; PRIORITY JOURNAL; PROGNOSIS; PULMONARY HYPERTENSION; RETROSPECTIVE STUDY; SEX DIFFERENCE; SURVIVAL TIME;

ACTIVIN RECEPTORS, TYPE II; ADOLESCENT; BONE MORPHOGENETIC PROTEIN RECEPTORS, TYPE II; CHILD; CHILD, PRESCHOOL; FEMALE; HUMANS; HYPERTENSION, PULMONARY; MALE; MUTATION; POLYMERASE CHAIN REACTION; PROGNOSIS; RETROSPECTIVE STUDIES; SURVIVAL RATE; TREATMENT OUTCOME; VASODILATOR AGENTS;

EID: 84864400689     PISSN: 00029149     EISSN: 18791913     Source Type: Journal    
DOI: 10.1016/j.amjcard.2012.04.035     Document Type: Article

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