Interferon gamma upregulates frataxin and corrects the functional deficits in a Friedreich ataxia model

Human Molecular Genetics

Volumn 21, Issue 13, 2012, Pages 2855-2861

  Tomassini, Barbara ^a   Arcuri, Gaetano ^a   Fortuni, Silvia ^a   Sandi, Chiranjeevi ^b   Ezzatizadeh, Vahid ^b   Casali, Carlo ^c   Condò, Ivano ^a   Malisan, Florence ^a   Al mahdawi, Sahar ^b   Pook, Mark ^b   Testi, Roberto ^a  

^a UNIVERSITY OF ROME TOR VERGATA   (Italy)

^b BRUNEL UNIVERSITY   (United Kingdom)

^c SAPIENZA UNIVERSITY OF ROME   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

FRATAXIN; GAMMA INTERFERON;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BASAL GANGLION; CONTROLLED STUDY; FEMALE; FRIEDREICH ATAXIA; FXN GENE; GENE; GENETIC TRANSCRIPTION; HUMAN; HUMAN CELL; IN VIVO STUDY; MALE; METABOLISM; MOUSE; NERVE CELL; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; SENSORIMOTOR FUNCTION; UPREGULATION;

ANIMALS; CELLS, CULTURED; DISEASE MODELS, ANIMAL; FRIEDREICH ATAXIA; GANGLIA, SPINAL; HELA CELLS; HUMANS; INTERFERON-GAMMA; IRON-BINDING PROTEINS; MICE; MICE, TRANSGENIC; MITOCHONDRIA; TRANSCRIPTION, GENETIC; TRANSCRIPTIONAL ACTIVATION;

MUS;

EID: 84863534984     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/dds110     Document Type: Article

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