Beta-glucosidase 1 (GBA1) is a second bile acid β-glucosidase in addition to β-glucosidase 2 (GBA2). Study in β-glucosidase deficient mice and humans

Biochemical and Biophysical Research Communications

Volumn 423, Issue 2, 2012, Pages 308-312

  Harzer, Klaus ^a   Blech Hermoni, Yotam ^b   Goldin, Ehud ^b   Felderhoff Mueser, Ursula ^c   Igney, Claudia ^d   Sidransky, Ellen ^b   Yildiz, Yildiz ^e  

^a UNIVERSITY OF TÜBINGEN   (Germany)

^b NATIONAL HUMAN GENOME RESEARCH INSTITUTE   (United States)

^c UNIVERSITY OF DUISBURG ESSEN   (Germany)

^d SIEMENS AG   (Germany)

^e UNIVERSITY HOSPITAL BONN   (Germany)

Author keywords

Glucosidase 2 (GBA2); Glucosidase null mice; Bile acid glucosidases; Glucosylceramide lipidosis; Isofagomine

Indexed keywords

BETA GLUCOSIDASE; BETA GLUCOSIDASE 1; BETA GLUCOSIDASE 2; BILE ACID CONJUGATE; GLUCOSYLCERAMIDASE; GLUCOSYLCERAMIDE; GLYCOSIDASE INHIBITOR; ISOFAGOMINE; RECOMBINANT PROTEIN; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL TISSUE; ARTICLE; BRAIN; CONTROLLED STUDY; ENZYME ACTIVITY; ENZYME DEFICIENCY; ENZYME SUBSTRATE; FIBROBLAST; HUMAN; HUMAN CELL; HUMAN TISSUE; HYDROLYSIS; LIVER; LYSOSOME; MOUSE; NONHUMAN; PRIORITY JOURNAL; WILD TYPE;

ANIMALS; BETA-GLUCOSIDASE; BILE ACIDS AND SALTS; BRAIN; FIBROBLASTS; GAUCHER DISEASE; GLUCOSIDES; HUMANS; HYDROLYSIS; LIVER; MALE; MICE;

MUS;

EID: 84862906125     PISSN: 0006291X     EISSN: 10902104     Source Type: Journal    
DOI: 10.1016/j.bbrc.2012.05.117     Document Type: Article

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