Management of the failing Fontan circulation

Heart

Volumn 98, Issue 14, 2012, Pages 1098-1104

  Deal, Barbara J ^a   Jacobs, Marshall L ^b  

^a NORTHWESTERN UNIVERSITY   (United States)

^b LERNER RESEARCH INSTITUTE   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

BETA ADRENERGIC RECEPTOR BLOCKING AGENT; VASODILATOR AGENT;

AORTOPULMONARY SHUNT; ASCITES; ATRIOVENTRICULAR BLOCK; BRONCHITIS; CONGENITAL HEART DISEASE; CYANOSIS; EXERCISE TEST; EXERCISE TOLERANCE; FONTAN PROCEDURE; HEALTH CARE QUALITY; HEART ARRHYTHMIA; HEART ATRIUM PACEMAKER; HEART ATRIUM PACING; HEART OUTFLOW TRACT OBSTRUCTION; HEART OUTPUT; HEART VENTRICLE FAILURE; HEART VENTRICLE FUNCTION; HEMODYNAMICS; HUMAN; LUNG CIRCULATION; LUNG VASCULAR RESISTANCE; OUTCOME ASSESSMENT; PRIORITY JOURNAL; REVIEW; SURGICAL MORTALITY; TREATMENT FAILURE; VALVULAR HEART DISEASE;

DISEASE MANAGEMENT; DISEASE PROGRESSION; FONTAN PROCEDURE; HEART DEFECTS, CONGENITAL; HEART TRANSPLANTATION; HUMANS; PATIENT SELECTION; PROGNOSIS; TREATMENT FAILURE;

EID: 84862873321     PISSN: 13556037     EISSN: 1468201X     Source Type: Journal    
DOI: 10.1136/heartjnl-2011-301133     Document Type: Review

References (20)

1. Fontan F, Baudet E. Surgical repair of tricuspid atresia. Thorax 1971;26:240-8. The surgery as described is obsolete, but worth reading for the comments on the longevity of homografts, perioperative management, and prediction of arrhythmias.
2. Hosein RB, Clarke AJ, McGuirk SP, et al. Factors influencing early and late outcome following the Fontan procedure in the current era. The 'Two Commandments'? Eur J Cardiothorac Surg 2007;31:344-53. An in-depth analysis of the key haemodynamic factors contributing to long term survival in a large series of Fontan patients. (Pubitemid 46329389)
3. d'Udekem Y, Iyengar AJ, Cochrane AD, et al. The Fontan procedure: contemporary techniques have improved long-term outcomes. Circulation 2007;116(11 Suppl):I157-64. An excellent comparison of the long term outcomes of patients undergoing the three major types of Fontan modifications. (Pubitemid 47480785)
4. Cohen MS, Zak V, Atz AM, et al. Anthropometric measures after Fontan procedure: implications for suboptimal functional outcome. Am Heart J 2010;160:1092-8.
5. Fernandes SM, McElhinney DB, Khairy P, et al. Serial cardiopulmonary exercise testing in patients with previous Fontan surgery. Pediatr Cardiol 2010;31:175-80.
6. Diller GP, Giardini A, Dimopoulos K, et al. Predictors of morbidity and mortality in contemporary Fontan patients: results from a multicenter study including cardiopulmonary exercise testing in 321 patients. Eur Heart J 2010;31:3073-83. An excellent multicentre study of exercise testing in adolescents and young adults with Fontan physiology, and analysis of factors correlating with poor outcomes.
7. Baek JS, Bae EJ, Ko JS, et al. Late hepatic complications after Fontan operation; non-invasive markers of hepatic fibrosis and risk factors. Heart 2010;96:1750-5. In-depth review of results of hepatic imaging and functional testing in a large number of older Fontan patients, with indices correlating with hepatic complications.
8. van den Bosch AE, Roos-Hesselink JW, van Domburg R, et al. Long-term outcome and quality of life in adult patients after the Fontan operation. Am J Cardiol 2004;93:1141-5. Although not a large number of patients, a thoughtful and comprehensive review of all complications encountered in a group of adult Fontan patients followed in a single centre. (Pubitemid 38521044)
9. Kim SJ, Kim WH, Lim HG, et al. Outcome of 200 patients after an extracardiac Fontan procedure. J Thorac Cardiovasc Surg 2008;136:108-16.
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12. Lee JR, Kwak J, Kim KC, et al. Comparison of lateral tunnel and extracardiac conduit Fontan procedure. Interact Cardiovasc Thorac Surg 2007;6:328-30.
13. Nurnberg JH, Ovroutski S, Alexi-Meskishvili V, et al. New onset arrhythmias after the extracardiac conduit Fontan operation compared with the intraatrial lateral tunnel procedure: early and midterm results. Ann Thorac Surg 2004;78:1979-88. (Pubitemid 39556273)
14. Yap SC, Harris L, Silversides CK, et al. Outcome of intra-atrial re-entrant tachycardia catheter ablation in adults with congenital heart disease. J Am Coll Cardiol 2010;56:1589-96. An excellent review of the outcomes of catheter ablation procedures for arrhythmias in adults with congenital heart disease, with discussion of factors associated with procedural success.
15. Mavroudis C, Backer CL, Deal BJ. Late reoperations for Fontan patients: state of the art invited review. Eur J Cardiothorac Surg 2008;34:1034-40. A detailed review of arrhythmia mechanisms, surgical techniques, anatomic variants, and discussion of outcomes in a large group of Fontan patients undergoing surgical conversion and arrhythmia surgery.
16. Mavroudis C, Deal BJ, Backer CL, et al. 111 Fontan conversions with arrhythmia surgery: surgical lessons and outcomes. Ann Thorac Surg 2007;84:1457-66. (Pubitemid 47593018)
17. Nakamura Y, Yagihara T, Kagisaki K, et al. Ventricular performance in long-term survivors after Fontan operation. Ann Thorac Surg 2011;91:172-80.
18. Khairy P, Fernandes SM, Mayer JE Jr, et al. Long-term survival, modes of death, and predictors of mortality in patients with Fontan surgery. Circulation 2008;117:85-92. An in-depth analysis of all-cause mortality in a large group of Fontan patients operated on in a single centre before 1985.
19. Davies RR, Chen JM, Mosca RS. The Fontan procedure: evolution in technique: attendant imperfections and transplantation for "failure". Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2011;14:55-66. An excellent discussion of the physiology of surgical Fontan modifications and long term complications, and review of outcomes from transplantation.
20. Bernstein D, Naftel D, Chin C, et al. Outcome of listing for cardiac transplantation for failed Fontan: a multi-institutional study. Circulation 2006;114:273-80. (Pubitemid 44297093)