Multiple dysplastic liver nodules in PFIC2 underscore risk for neoplasia associated with functional BSEP deficiency

American Journal of Surgical Pathology

Volumn 36, Issue 5, 2012, Pages 785-786

  Sheridan, Rachel M ^a   Gupta, Anita ^a   Miethke, Alexander ^a   Knisely, Alexander S ^b   Bove, Kevin E ^a  

^a CINCINNATI CHILDREN'S HOSPITAL MEDICAL CENTER   (United States)

^b KING S COLLEGE HOSPITAL   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

ABC TRANSPORTER; ABCB11 PROTEIN, HUMAN; BIOLOGICAL MARKER;

ADOLESCENT; CASE REPORT; GENETIC MARKER; GENETICS; HUMAN; INTRAHEPATIC CHOLESTASIS; LETTER; LIVER TUMOR; METABOLISM; RISK;

ADOLESCENT; ATP-BINDING CASSETTE TRANSPORTERS; BIOLOGICAL MARKERS; CHOLESTASIS, INTRAHEPATIC; GENETIC MARKERS; HUMANS; LIVER NEOPLASMS; RISK;

EID: 84859921529     PISSN: 01475185     EISSN: 15320979     Source Type: Journal    
DOI: 10.1097/PAS.0b013e3182500c35     Document Type: Letter

References (6)

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5. Strautnieks SS, Byrne JA, Pawlikowska L, et al. Severe bile salt export pump deficiency: 82 different ABCB11 mutations in 109 families. Gastroenterology. 2008; 134: 1203-1214.
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