Propionic acidemia: To liver transplant or not to liver transplant?

Pediatric Transplantation

Volumn 16, Issue 3, 2012, Pages 209-210

  Chapman, Kimberly A ^a   Summar, Marshall L ^a   Enns, Gregory M ^b  

^a CHILDREN'S NATIONAL MEDICAL CENTER   (United States)

^b STANFORD UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

METHYLMALONYL COENZYME A CARBOXYLTRANSFERASE; PROPIONYL COENZYME A CARBOXYLASE;

CARDIOMYOPATHY; COMA; DISORDERS OF MITOCHONDRIAL FUNCTIONS; EDITORIAL; ENZYME ACTIVITY; FOLLOW UP; HEART FUNCTION; HETEROZYGOTE; HUMAN; HYPERAMMONEMIA; LETHARGY; LIVER TRANSPLANTATION; LIVING DONOR; MAPLE SYRUP URINE DISEASE; MEAT; METABOLIC ACIDOSIS; MORBIDITY; MORTALITY; NEUROLOGICAL COMPLICATION; PROPIONIC ACIDEMIA; RETROSPECTIVE STUDY; SURVIVAL RATE; UREA CYCLE DISORDER;

CHILD; GRAFT SURVIVAL; HETEROZYGOTE; HUMANS; LIVER TRANSPLANTATION; POSTOPERATIVE COMPLICATIONS; PROPIONIC ACIDEMIA; TREATMENT OUTCOME;

EID: 84859717317     PISSN: 13973142     EISSN: 13993046     Source Type: Journal    
DOI: 10.1111/j.1399-3046.2012.01649.x     Document Type: Editorial

References (11)

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