Desmoplastic small round cell tumors with EWS-WT1 fusion transcript in children and young adults

Pediatric Blood and Cancer

Volumn 58, Issue 6, 2012, Pages 891-897

  Philippe Chomette, Pascale ^a   Kabbara, Nabil ^b   Andre, Nicolas ^c   Pierron, Gaelle ^b   Coulomb, Aurore ^d   Laurence, Valérie ^b   Blay, Jean Yves ^e   Delattre, Olivier ^b   Schleiermacher, Gudrun ^b   Orbach, Daniel ^b  

^a HÔPITAL ROBERT DEBRÉ   (France)

^b INSTITUT CURIE   (France)

^c TIMONE HOSPITAL   (France)

^d ARMAND TROUSSEAU HOSPITAL   (France)

^e CENTRE LÉON BÉRARD   (France)

Author keywords

Adolescent young adult; Desmoplastic small round cell tumor; EWS WT1 gene fusion transcript; Extensive surgery; High dose chemotherapy; Sarcoma

Indexed keywords

BLEOMYCIN; CARBOPLATIN; CISPLATIN; CYCLOPHOSPHAMIDE; DACARBAZINE; DACTINOMYCIN; DOXORUBICIN; EPIRUBICIN; ETOPOSIDE; EWS WT1 FUSION PROTEIN; HYBRID PROTEIN; IFOSFAMIDE; NAVELBINE; RNA BINDING PROTEIN EWS; UNCLASSIFIED DRUG; VINCRISTINE; WT1 PROTEIN;

ADOLESCENT; ADULT; ARTICLE; CANCER COMBINATION CHEMOTHERAPY; CANCER LOCALIZATION; CANCER RADIOTHERAPY; CANCER SURGERY; CANCER SURVIVAL; CHILD; CHILDHOOD CANCER; CLINICAL ARTICLE; DESMOPLASTIC SMALL ROUND CELL TUMOR; DRUG MEGADOSE; EVENT FREE SURVIVAL; FEMALE; HUMAN; MALE; OVERALL SURVIVAL; PRESCHOOL CHILD; PRIORITY JOURNAL; PROTEIN EXPRESSION; RETROSPECTIVE STUDY; SCHOOL CHILD; SURVIVAL RATE; SURVIVAL TIME;

ADOLESCENT; ADULT; ANTINEOPLASTIC COMBINED CHEMOTHERAPY PROTOCOLS; CHILD; CHILD, PRESCHOOL; COMBINED MODALITY THERAPY; DESMOPLASTIC SMALL ROUND CELL TUMOR; DISEASE-FREE SURVIVAL; FEMALE; HUMANS; KAPLAN-MEIER ESTIMATE; MALE; ONCOGENE PROTEINS, FUSION; RADIOTHERAPY; REAL-TIME POLYMERASE CHAIN REACTION; RETROSPECTIVE STUDIES; REVERSE TRANSCRIPTASE POLYMERASE CHAIN REACTION; TREATMENT OUTCOME; YOUNG ADULT;

EID: 84858693604     PISSN: 15455009     EISSN: 15455017     Source Type: Journal    
DOI: 10.1002/pbc.23403     Document Type: Article

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