-
1
-
-
0024423668
-
Identification of the cystic fibrosis gene: Genetic analysis
-
Kerem B, Rommens JM, Buchanan JA, Markiewicz D, Cox TK, Chakravarti A, Buchwald M, Tsui LC. Identification of the cystic fibrosis gene: genetic analysis. Science 1989;245:1073-1080. (Pubitemid 19231815)
-
(1989)
Science
, vol.245
, Issue.4922
, pp. 1073-1080
-
-
Kerem, B.-S.1
Rommens, J.M.2
Buchanan, J.A.3
Markiewicz, D.4
Cox, T.K.5
Chakravarti, A.6
Buchwald, M.7
Tsui, L.-C.8
-
2
-
-
0032433707
-
Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease
-
DOI 10.1016/S0092-8674(00)81724-9
-
Matsui H, Grubb BR, Tarran R, Randell SH, Gatzy JT, Davis CW, Boucher RC. Evidence for periciliary liquid layer depletion, not abnormal ion composition, in the pathogenesis of cystic fibrosis airways disease. Cell 1998;95:1005-1015. (Pubitemid 29019052)
-
(1998)
Cell
, vol.95
, Issue.7
, pp. 1005-1015
-
-
Matsui, H.1
Grubb, B.R.2
Tarran, R.3
Randell, S.H.4
Gatzy, J.T.5
Davis, C.W.6
Boucher, R.C.7
-
4
-
-
30944452384
-
Mucus clearance and lung function in cystic fibrosis with hypertonic saline
-
DOI 10.1056/NEJMoa043891
-
Donaldson SH, Bennett WD, Zeman KL, Knowles MR, Tarran R, Boucher RC. Mucus clearance and lung function in cystic fibrosis with hypertonic saline. N Engl J Med 2006;354:241-250. (Pubitemid 43113029)
-
(2006)
New England Journal of Medicine
, vol.354
, Issue.3
, pp. 241-250
-
-
Donaldson, S.H.1
Bennett, W.D.2
Zeman, K.L.3
Knowles, M.R.4
Tarran, R.5
Boucher, R.C.6
-
5
-
-
30944466084
-
A controlled trial of long-term inhaled hypertonic saline in patients with cystic fibrosis
-
DOI 10.1056/NEJMoa043900
-
Elkins MR, Robinson M, Rose BR, Harbour C, Moriarty CP, Marks GB, Belousova EG, Xuan W, Bye PT. A controlled trial of long-term inhaled hypertonic saline in patients with cystic fibrosis. N Engl J Med 2006;354:229-240. (Pubitemid 43113028)
-
(2006)
New England Journal of Medicine
, vol.354
, Issue.3
, pp. 229-240
-
-
Elkins, M.R.1
Robinson, M.2
Rose, B.R.3
Harbour, C.4
Moriarty, C.P.5
Marks, G.B.6
Belousova, E.G.7
Xuan, W.8
Bye, P.T.P.9
-
6
-
-
0031444391
-
Inhalation of dry-powder mannitol increases mucociliary clearance
-
DOI 10.1183/09031936.97.10112449
-
Daviskas E, Anderson SD, Brannan JD, Chan HK, Eberl S, Bautovich G. Inhalation of dry-powder mannitol increases mucociliary clearance. Eur Respir J 1997;10:2449-2454. (Pubitemid 28048614)
-
(1997)
European Respiratory Journal
, vol.10
, Issue.11
, pp. 2449-2454
-
-
Daviskas, E.1
Anderson, S.D.2
Brannan, J.D.3
Chan, H.-K.4
Eberl, S.5
Bautovich, G.6
-
7
-
-
44649166466
-
Inhaled mannitol improves lung function in cystic fibrosis
-
DOI 10.1378/chest.07-2294
-
Jaques A, Daviskas E, Turton JA, McKay K, Cooper P, Stirling RG, Robertson CF, Bye PT, Lesouef PN, Shadbolt B, et al. Inhaled mannitol improves lung function in cystic fibrosis. Chest 2008;133:1388-1396. (Pubitemid 351892995)
-
(2008)
Chest
, vol.133
, Issue.6
, pp. 1388-1396
-
-
Jaques, A.1
Daviskas, E.2
Turton, J.A.3
McKay, K.4
Cooper, P.5
Stirling, R.G.6
Robertson, C.F.7
Bye, P.T.P.8
LeSouef, P.N.9
Shadbolt, B.10
Anderson, S.D.11
Charlton, B.12
-
8
-
-
78651452280
-
Inhaled mannitol in patients with cystic fibrosis: A randomised open-label dose response trial
-
Teper A, Jaques A, Charlton B. Inhaled mannitol in patients with cystic fibrosis: a randomised open-label dose response trial. J Cystic Fibrosis 2011;10:1-8.
-
(2011)
J Cystic Fibrosis
, vol.10
, pp. 1-8
-
-
Teper, A.1
Jaques, A.2
Charlton, B.3
-
9
-
-
80355127141
-
Inhaled dry powder mannitol in cystic fibrosis: An efficacy and safety study
-
Bilton D, Robinson P, Cooper P, Gallagher CG, Kolbe J, Fox H, Jaques A, Charlton B. Inhaled dry powder mannitol in cystic fibrosis: an efficacy and safety study. Eur Respir J 2011;38:1071-1080.
-
(2011)
Eur Respir J
, vol.38
, pp. 1071-1080
-
-
Bilton, D.1
Robinson, P.2
Cooper, P.3
Gallagher, C.G.4
Kolbe, J.5
Fox, H.6
Jaques, A.7
Charlton, B.8
-
10
-
-
84858234304
-
Long-term inhaled dry powder mannitol in cystic fibrosis: An international randomized study
-
Aitken M, Bellon G, De Boeck K, Flume PA, Fox HG, Geller DE, Haarman EG, Hebetreit HU, Lapey A, Manjula Schou I, et al. Long-term inhaled dry powder mannitol in cystic fibrosis: an international randomized study. Am J Respir Crit Care Med 2012;185:645-652.
-
(2012)
Am J Respir Crit Care Med
, vol.185
, pp. 645-652
-
-
Aitken, M.1
Bellon, G.2
De Boeck, K.3
Flume, P.A.4
Fox, H.G.5
Geller, D.E.6
Haarman, E.G.7
Hebetreit, H.U.8
Lapey, A.9
Manjula Schou, I.10
-
11
-
-
0028129568
-
Effect of aerosolized recombinant human DNase on exacerbations of respiratory symptoms and on pulmonary function in patients with cystic fibrosis
-
DOI 10.1056/NEJM199409083311003
-
Fuchs HJ, Borowitz DS, Christiansen DH, Morris EM, Nash ML, Ramsey BW, Rosenstein BJ, Smith AL, Wohl ME. Effect of aerosolized recombinant human DNase on exacerbations of respiratory symptoms and on pulmonary function in patients with cystic fibrosis: the Pulmozyme Study Group. N Engl J Med 1994;331:637-642. (Pubitemid 24276863)
-
(1994)
New England Journal of Medicine
, vol.331
, Issue.10
, pp. 637-642
-
-
Fuchs, H.J.1
Borowitz, D.S.2
Christiansen, D.H.3
Morris, E.M.4
Nash, M.L.5
Ramsey, B.W.6
Rosenstein, B.J.7
Smith, A.L.8
Wohl, M.E.9
-
13
-
-
80455162465
-
A CFTR potentiator in patients with cystic fibrosis and the G551D mutation
-
Ramsey BW, Davies J, McElvaney NG, Tullis E, Bell SC, Drevinek P, Griese M, McKone EF, Wainwright CE, Konstan MW, et al. A CFTR potentiator in patients with cystic fibrosis and the G551D mutation. N Engl J Med 2011;365:1663-1672.
-
(2011)
N Engl J Med
, vol.365
, pp. 1663-1672
-
-
Ramsey, B.W.1
Davies, J.2
McElvaney, N.G.3
Tullis, E.4
Bell, S.C.5
Drevinek, P.6
Griese, M.7
McKone, E.F.8
Wainwright, C.E.9
Konstan, M.W.10
|