Progressive neuronal inclusion formation and axonal degeneration in CHMP2B mutant transgenic mice

Brain

Volumn 135, Issue 3, 2012, Pages 819-832

  Ghazi Noori, Shabnam ^a   Froud, Kristina E ^a   Mizielinska, Sarah ^a   Powell, Caroline ^a   Smidak, Michelle ^a   Fernandez De Marco, Mar ^a   O'Malley, Catherine ^a   Farmer, Michael ^a   Parkinson, Nick ^a   Fisher, Elizabeth M C ^a   Asante, Emmanuel A ^a   Brandner, Sebastian ^a   Collinge, John ^a   Isaacs, Adrian M ^a  

^a UNIVERSITY COLLEGE LONDON   (United Kingdom)

Author keywords

CHMP2B; ESCRT; frontotemporal dementia; transgenic mice

Indexed keywords

AMYLOID PRECURSOR PROTEIN; CHARGED MULTIVESICULAR BODY PROTEIN 2B; ESCRT PROTEIN; FUSED IN SARCOMA PROTEIN; MUTANT PROTEIN; PROTEIN; PROTEIN P62; TAR DNA BINDING PROTEIN; UBIQUITIN; UNCLASSIFIED DRUG;

AGING; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BRAIN STEM; CARBOXY TERMINAL SEQUENCE; CELL INCLUSION; CELL SWELLING; CONTROLLED STUDY; CORPUS CALLOSUM; DEMENTIA; EXPERIMENTAL MODEL; FEMALE; FRONTAL CORTEX; GENE EXPRESSION; GENE MUTATION; GLIOSIS; KNOCKOUT MOUSE; MALE; MOUSE; MOUSE MUTANT; NERVE CELL INCLUSION; NERVE FIBER DEGENERATION; NEUROPATHOLOGY; NEUROPATHY; NONHUMAN; PRIORITY JOURNAL; SPINAL CORD; SURVIVAL; THALAMUS; TRANSGENIC MOUSE; WILD TYPE;

EID: 84857568926     PISSN: 00068950     EISSN: 14602156     Source Type: Journal    
DOI: 10.1093/brain/aws006     Document Type: Article

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