Role of a disordered steroid metabolome in the elucidation of sterol and steroid biosynthesis

Lipids

Volumn 47, Issue 1, 2012, Pages 1-12

  Shackleton, Cedric H L ^a,b  

^a UNIVERSITY OF BIRMINGHAM   (United Kingdom)

^b CHILDREN S HOSPITAL OAKLAND RESEARCH INSTITUTE   (United States)

Author keywords

Cholesterol synthesis; Steroid biosynthesis; Steroid metabolism

Indexed keywords

3ALPHA(OR 20BETA) HYDROXYSTEROID DEHYDROGENASE; 7 DEHYDROCHOLESTEROL; CHOLESTEROL; CYTOCHROME P450 REDUCTASE; ESTRADIOL; LANOSTEROL; OXIDOREDUCTASE; PARVOVIRUS VECTOR; STEROID; STEROID HORMONE; STEROL;

ADENOVIRUS; CHOLESTEROL DIET; CHOLESTEROL SYNTHESIS; CONGENITAL ADRENAL HYPERPLASIA; CORTISONE REDUCTASE DEFICIENCY; DIAGNOSTIC ACCURACY; DIET SUPPLEMENTATION; DISEASE SEVERITY; DISORDERS OF STEROID METABOLISM; ENZYME ACTIVE SITE; ENZYME DEFICIENCY; HUMAN; METABOLOMICS; NONHUMAN; OXIDATION; OXIDATION REDUCTION REACTION; P450 OXIDOREDUCTASE DEFICIENCY; PATHOGENESIS; REVIEW; SMITH LEMLI OPITZ SYNDROME; STEROID URINE LEVEL; STEROIDOGENESIS; THIN LAYER CHROMATOGRAPHY; VIRAL GENE THERAPY; VIRUS RECOMBINANT;

11-BETA-HYDROXYSTEROID DEHYDROGENASES; 46, XX DISORDERS OF SEX DEVELOPMENT; ADRENAL GLANDS; ADRENOGENITAL SYNDROME; ANIMALS; HIRSUTISM; HUMANS; LIPOGENESIS; METABOLOME; MICE; MUTATION; OXIDOREDUCTASES; OXIDOREDUCTASES ACTING ON CH-CH GROUP DONORS; PREGNANETRIOL; SMITH-LEMLI-OPITZ SYNDROME; STEROID METABOLISM, INBORN ERRORS; STEROLS;

MURINAE;

EID: 84857052729     PISSN: 00244201     EISSN: 15589307     Source Type: Journal    
DOI: 10.1007/s11745-011-3605-6     Document Type: Review

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