Clinical features of congenital portosystemic shunt in children

European Journal of Pediatrics

Volumn 171, Issue 2, 2012, Pages 395-400

  Kim, Myung Jin ^a   Ko, Jae Sung ^a,b   Seo, Jeong Kee ^a   Yang, Hye Ran ^a   Chang, Ju Young ^a   Kim, Gi Beom ^a   Cheon, Jung Eun ^a   Kim, Woo Sun ^a  

^a Seoul National University   (South Korea)

^b Seoul National University Children's Hospital   (South Korea)

Author keywords

Congenital portosystemic shunt; Embolization; Galactosemia; Hyperammonemia; Pulmonary hypertension

Indexed keywords

BOSENTAN; SILDENAFIL;

ABDOMINAL PAIN; ARTIFICIAL EMBOLISM; ATTENTION DEFICIT DISORDER; CLINICAL ARTICLE; CLINICAL FEATURE; CONGENITAL PORTOSYSTEMIC SHUNT; ECHOCARDIOGRAPHY; FEMALE; FETUS; FETUS ECHOGRAPHY; GALACTOSEMIA; HEART ATRIUM SEPTUM DEFECT; HEPATIC ENCEPHALOPATHY; HUMAN; HYPERAMMONEMIA; INFANT; INTRAUTERINE GROWTH RETARDATION; MALE; MENTAL DEFICIENCY; NUCLEAR MAGNETIC RESONANCE IMAGING; OBSTRUCTIVE JAUNDICE; PRIORITY JOURNAL; PULMONARY HYPERTENSION; REVIEW; SPLENOMEGALY; TREATMENT OUTCOME;

CHILD; CHILD, PRESCHOOL; EMBOLIZATION, THERAPEUTIC; FEMALE; FOLLOW-UP STUDIES; HEPATIC VEINS; HUMANS; INFANT; INFANT, NEWBORN; MALE; PORTAL VEIN; VASCULAR MALFORMATIONS; VENA CAVA, INFERIOR;

EID: 84857049233     PISSN: 03406199     EISSN: 14321076     Source Type: Journal    
DOI: 10.1007/s00431-011-1564-9     Document Type: Review

References (19)

1. L Delle Chiaie P Neuberger T Von Kalle 2008 Congenital intrahepatic portosystemic shunt: prenatal diagnosis and possible influence on fetal growth Ultrasound Obstet Gynecol 32 233 235 18663772 10.1002/uog.6116 1:STN:280:DC%2BD1cvptlGqsg%3D%3D
2. WN Evans A Galindo RJ Acherman A Rothman DP Berthoty 2009 Congenital portosystemic shunts and AMPLATZER vascular plug occlusion in newborns Pediatr Cardiol 30 1083 1088 19629574 10.1007/s00246-009-9501-7
3. GB Ferrero F Porta E Biamino A Mussa E Garelli F Chiappe A Veltri MC Silengo F Gennari 2010 Remittent hyperammonemia in congenital portosystemic shunt Eur J Pediatr 169 369 372 19618212 10.1007/s00431-009-1031-z
4. S Franchi-Abella S Branchereau V Lambert M Fabre C Steimberg J Losay JY Riou D Pariente F Gauthier E Jacquemin O Bernard 2010 Complications of congenital portosystemic shunts in children: therapeutic options and outcomes J Pediatr Gastroenterol Nutr 51 322 330 20601902
5. R Gitzelmann I Forster UV Willi 1997 Hypergalactosaemia in a newborn: self-limiting intrahepatic portosystemic venous shunt Eur J Pediatr 156 719 722 9296538 10.1007/s004310050698 1:STN:280:DyaK2svktFWjsg%3D%3D (Pubitemid 27377461)
6. S Kamata Y Kitayama N Usui S Kuroda K Nose T Sawai A Okada 2000 Patent ductus venosus with a hypoplastic intrahepatic portal system presenting intrapulmonary shunt: a case treated with banding of the ductus venosus J Pediatr Surg 35 655 657 10770411 10.1053/jpsu.2000.0350657 1:STN:280: DC%2BD3c3jtFWrsg%3D%3D (Pubitemid 30181057)
7. T Kono T Hiki S Kuwashima T Hashimoto Y Kaji 2009 Hypergalactosemia in early infancy: diagnostic strategy with an emphasis on imaging Pediatr Int 51 276 282 19405932 10.1111/j.1442-200X.2008.02692.x
8. Konstas AA, Digumarthy SR, Avery LL, Wallace KL, Lisovsky M, Misdraji J, Hahn PF (2010) Congenital portosystemic shunts: imaging findings and clinical presentations in 11 patients. Eur J Radiol [Epub ahead of print]
9. TB Lautz N Tantemsapya E Rowell RA Superina 2011 Management and classification of type II congenital portosystemic shunts J Pediatr Surg 46 308 314 21292079 10.1016/j.jpedsurg.2010.11.009
10. Y Nishimura G Tajima A Dwi Bahagia A Sakamoto H Ono N Sakura K Naito M Hamakawa C Yoshii M Kubota K Kobayashi T Saheki 2004 Differential diagnosis of neonatal mild hypergalactosaemia detected by mass screening: clinical significance of portal vein imaging J Inherit Metab Dis 27 11 18 14970742 10.1023/B:BOLI.0000016621.29854.d6 1:CAS:528:DC%2BD2cXhtlWrtbk%3D (Pubitemid 38418191)
11. B Oguz D Akata F Balkanci O Akhan 2003 Intrahepatic portosystemic venous shunt: diagnosis by colour/power Doppler imaging and three-dimensional ultrasound Br J Radiol 76 487 490 12857710 10.1259/bjr/65168282 1:STN:280:DC%2BD3szislKruw%3D%3D (Pubitemid 36903365)
12. T Ohno J Muneuchi K Ihara T Yuge Y Kanaya S Yamaki T Hara 2008 Pulmonary hypertension in patients with congenital portosystemic venous shunt: a previously unrecognized association Pediatrics 121 e892 899 18362102 10.1542/peds.2006-3411
13. H Ono H Mawatari N Mizoguchi T Eguchi N Sakura 1998 Clinical features and outcome of eight infants with intrahepatic porto-venous shunts detected in neonatal screening for galactosaemia Acta Paediatr 87 631 634 9686654 10.1111/j.1651-2227.1998.tb01521.x 1:STN:280:DyaK1czkvFCnsQ%3D%3D (Pubitemid 28331048)
14. JH Park SH Cha JK Han MC Han 1990 Intrahepatic portosystemic venous shunt AJR Am J Roentgenol 155 527 528 2117349 1:STN:280:DyaK3czltVKitg%3D%3D (Pubitemid 20254494)
15. N Sakura N Mizoguchi T Eguchi H Ono H Mawatari K Naitou K Ito 1997 Elevated plasma bile acids in hypergalactosaemic neonates: a diagnostic clue to portosystemic shunts Eur J Pediatr 156 716 718 9296537 10.1007/s004310050697 1:CAS:528:DyaK2sXlvFyktrY%3D (Pubitemid 27377460)
16. MD Stringer 2008 The clinical anatomy of congenital portosystemic venous shunts Clin Anat 21 147 157 18161055 10.1002/ca.20574 (Pubitemid 351358478)
17. Y Takehara K Mori T Edagawa M Sugimoto H Takehara M Ito Y Kuroda 2004 Presumed hypoplastic intrahepatic portal system due to patent ductus venosus: importance of direct occlusion test of ductus venosus under open laparotomy Pediatr Int 46 484 486 15310321 10.1111/j.1442-200x.2004.01914.x (Pubitemid 39119169)
18. S Tanoue H Kiyosue E Komatsu Y Hori T Maeda H Mori 2003 Symptomatic intrahepatic portosystemic venous shunt: embolization with an alternative approach AJR Am J Roentgenol 181 71 78 12818832 (Pubitemid 36741463)
19. T Uchino I Matsuda F Endo 1999 The long-term prognosis of congenital portosystemic venous shunt J Pediatr 135 254 256 10431123 10.1016/S0022-3476(99) 70031-4 1:STN:280:DyaK1Mzmt1Gntw%3D%3D (Pubitemid 30180544)