Hyper-IgM, neutropenia, mild infections and low response to polyclonal stimulation: Hyper-IgM syndrome or common variable immunodeficiency?

International Journal of Immunopathology and Pharmacology

Volumn 24, Issue 4, 2011, Pages 983-991

  Rosado, M M ^a   Picchianti Diamanti, A ^b   Cascioli, S ^a   Ceccarelli, S ^a   Caporuscio, S ^b   D'Amelio, R ^b   Carsetti, R ^a   Lagana B ^b  

^a BAMBINO GESÙ CHILDREN S HOSPITAL   (Italy)

^b SAPIENZA UNIVERSITY OF ROME   (Italy)

Author keywords

Class switch recombination; Common variable immunodeficiency; Hyper IgM syndrome; Intravenous immunoglobulin

Indexed keywords

ACTIVATION INDUCED CYTIDINE DEAMINASE; CD40 ANTIGEN; CD40 LIGAND; CYCLOSPORIN A; IMMUNOGLOBULIN; IMMUNOGLOBULIN M; MESSENGER RNA; URACIL DNA GLYCOSIDASE; B CELL ACTIVATING FACTOR; C REACTIVE PROTEIN; CD19 ANTIGEN; CD22 ANTIGEN; CD24 ANTIGEN; CD27 ANTIGEN; CD3 ANTIGEN; CD38 ANTIGEN; CD4 ANTIGEN; CD45RO ANTIGEN; CD8 ANTIGEN; FILGRASTIM; FOLIC ACID; IMMUNOGLOBULIN G ANTIBODY; PREDNISONE; TETANUS ANTIBODY; TOLL LIKE RECEPTOR 9;

ADULT; ARTICLE; B LYMPHOCYTE; CASE REPORT; COMMON VARIABLE IMMUNODEFICIENCY; CONTROLLED STUDY; FEMALE; FEVER; HUMAN; HUMAN CELL; HYPER IGM SYNDROME; MULTIPLE CYCLE TREATMENT; MYALGIA; NEUTROPENIA; OUTCOME ASSESSMENT; POLYARTHRITIS; POLYCLONAL ACTIVATION; PRIORITY JOURNAL; RECURRENT INFECTION; RESPIRATORY TRACT INFECTION; T LYMPHOCYTE; ANTIBIOTIC THERAPY; ANTIBODY PRODUCTION; ANTIBODY SECRETING CELL; ANTIBODY TITER; ASTHENIA; CPG ISLAND; DRUG EFFICACY; ERYTHROCYTE SEDIMENTATION RATE; GENETIC RECOMBINATION; LYMPHOCYTE COUNT; LYMPHOCYTE PROLIFERATION; NAIL INFECTION; NEUTROPHIL COUNT; PERIPHERAL LYMPHOCYTE; REGULATORY T LYMPHOCYTE; UPREGULATION;

EID: 84856576660     PISSN: 03946320     EISSN: None     Source Type: Journal    
DOI: 10.1177/039463201102400416     Document Type: Article

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