A cellular model for the investigation of Fuchs' Endothelial Corneal Dystrophy

Experimental Eye Research

Volumn 93, Issue 6, 2011, Pages 880-888

  Kelliher, Clare ^a   Chakravarti, Shukti ^b   Vij, Neeraj ^b   Mazur, Steve ^b   Stahl, Patrick J ^c   Engler, Christoph ^a   Matthaei, Mario ^a   Yu, S Michael ^c   Jun, Albert S ^a  

^a JOHNS HOPKINS UNIVERSITY   (United States)

^b DEPARTMENT OF PATHOLOGY   (United States)

^c Johns Hopkins University   (United States)

Author keywords

Collagen mimetic peptides; Collagen VIII; Corneal endothelium; Fuchs' Endothelial Corneal Dystrophy

Indexed keywords

ACTIN; COLLAGEN TYPE 8; COLLAGEN TYPE VIII ALPHA2; COMPLEMENTARY DNA; MONOMER; MUTANT PROTEIN; UNCLASSIFIED DRUG;

ALLELE; ARTICLE; BIOACCUMULATION; COMPUTER MODEL; CORNEA DYSTROPHY; FUCHS ENDOTHELIAL CORNEAL DYSTROPHY; GENETIC TRANSFECTION; GENOTYPE; HUMAN; HUMAN CELL; IMMUNOFLUORESCENCE; MUTANT; MUTATION; PHENOTYPE; PRIORITY JOURNAL; THERMOSTABILITY; WESTERN BLOTTING; WILD TYPE;

ANIMALS; BLOTTING, WESTERN; CELLS, CULTURED; CHO CELLS; CIRCULAR DICHROISM; COLLAGEN TYPE VIII; COMPUTER SIMULATION; CRICETINAE; CRICETULUS; FLUORESCENT ANTIBODY TECHNIQUE; FUCHS' ENDOTHELIAL DYSTROPHY; GENETIC PREDISPOSITION TO DISEASE; HUMANS; MODELS, MOLECULAR; MOLECULAR MIMICRY; MUTAGENESIS, SITE-DIRECTED; MUTATION; PEPTIDES; PHENOTYPE; PROTEIN MULTIMERIZATION; PROTEIN STABILITY; RECOMBINANT PROTEINS; STRUCTURE-ACTIVITY RELATIONSHIP; TEMPERATURE; TRANSFECTION;

EID: 84855916773     PISSN: 00144835     EISSN: 10960007     Source Type: Journal    
DOI: 10.1016/j.exer.2011.10.001     Document Type: Article

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