Distinct neuropsychological profiles correspond to distribution of cortical thinning in inherited prion disease caused by insertional mutation

Journal of Neurology, Neurosurgery and Psychiatry

Volumn 83, Issue 1, 2012, Pages 109-114

  Alner, K ^a   Hyare, H ^a,b   Mead, S ^a,b   Rudge, P ^a,b   Wroe, S ^a,b   Rohrer, J D ^b   Ridgway, G R ^b   Ourselin, S ^b,c   Clarkson, M ^b,c   Hunt, H ^a   Fox, N C ^b   Webb, T ^a,b   Collinge, J ^a,b   Cipolotti, L ^a  

^a NATIONAL HOSPITAL FOR NEUROLOGY AND NEUROSURGERY   (United Kingdom)

^b UNIVERSITY COLLEGE LONDON   (United Kingdom)

^c UNIVERSITY COLLEGE LONDON   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

OCTAPEPTIDE; PRION PROTEIN;

ADULT; ARTICLE; BRAIN CORTEX; CLINICAL ARTICLE; CLINICAL ASSESSMENT; CLINICAL FEATURE; COGNITION; CONTROLLED STUDY; FEMALE; FRONTAL LOBE; GENE EXPRESSION REGULATION; GENE INSERTION; GENE MUTATION; GENETIC SCREENING; HUMAN; IMAGE ANALYSIS; MALE; MISSENSE MUTATION; NEUROPSYCHOLOGICAL TEST; NUCLEAR MAGNETIC RESONANCE IMAGING; OCCIPITAL LOBE; PARIETAL LOBE; PRION DISEASE; PRIORITY JOURNAL; UNITED KINGDOM;

ADULT; BRAIN; COGNITION DISORDERS; EXECUTIVE FUNCTION; FEMALE; GREAT BRITAIN; HUMANS; MAGNETIC RESONANCE IMAGING; MALE; MEMORY DISORDERS; MIDDLE AGED; MUTAGENESIS, INSERTIONAL; NEUROIMAGING; NEUROPSYCHOLOGICAL TESTS; PRION DISEASES; PRIONS; YOUNG ADULT;

EID: 84155165343     PISSN: 00223050     EISSN: 1468330X     Source Type: Journal    
DOI: 10.1136/jnnp-2011-300167     Document Type: Article

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