QTc prolongation and family history of sudden death in a patient with desmin cardiomyopathy

PACE - Pacing and Clinical Electrophysiology

Volumn 34, Issue 12, 2011, Pages

  Sung, Raphael K ^a   Ursell, Philip C ^a   Rame, J Eduardo ^b   Bailey, Helen ^a   Caleshu, Colleen ^a   Nussbaum, Robert L ^a   Scheinman, Melvin M ^a  

^a UNIVERSITY OF CALIFORNIA   (United States)

^b UNIVERSITY OF PENNSYLVANIA   (United States)

Author keywords

Congestive heart failure; Defibrillation ICD; Long QT

Indexed keywords

CONNEXIN 43; CREATINE KINASE; DESMIN; FERRITIN; IRON; LOOP DIURETIC AGENT; SODIUM CHANNEL NAV1.5;

ADULT; ARTICLE; BLOOD CELL COUNT; CARDIOMYOPATHY; CARDIOVASCULAR MAGNETIC RESONANCE; CASE REPORT; CESAREAN SECTION; CHORIOAMNIONITIS; CONGESTIVE HEART FAILURE; CREATINE KINASE BLOOD LEVEL; DEFIBRILLATOR; DESMIN CARDIOMYOPATHY; DISEASE EXACERBATION; DIURESIS; DYSPNEA; ECHOCARDIOGRAPHY; ELECTROCARDIOGRAM; ELECTRON MICROSCOPY; EXON; FAMILY HISTORY; FATIGUE; FEMALE; FERRITIN BLOOD LEVEL; FIBROSING ALVEOLITIS; FOLLOW UP; GENETIC POLYMORPHISM; GENETIC SCREENING; GENOTYPE; HEART CATHETERIZATION; HEART ELECTROPHYSIOLOGY; HEART MUSCLE BIOPSY; HEART RATE; HEART VENTRICLE HYPERTROPHY; HISTOPATHOLOGY; HUMAN; IMMUNOLOCALIZATION; INTRON; IRON BLOOD LEVEL; MISSENSE MUTATION; MONGOLIA; PHENOTYPIC VARIATION; PROTEIN ELECTROPHORESIS; QT PROLONGATION; SUDDEN DEATH;

ADULT; DEATH, SUDDEN, CARDIAC; DEFIBRILLATORS, IMPLANTABLE; DESMIN; ELECTROCARDIOGRAPHY; ELECTROPHYSIOLOGIC TECHNIQUES, CARDIAC; ETHER-A-GO-GO POTASSIUM CHANNELS; EXONS; FEMALE; HEART FAILURE; HUMANS; LONG QT SYNDROME; MUTATION; MYOSITIS, INCLUSION BODY; PREGNANCY; PREGNANCY COMPLICATIONS, CARDIOVASCULAR; SODIUM CHANNELS; TREATMENT OUTCOME;

EID: 83455179742     PISSN: 01478389     EISSN: 15408159     Source Type: Journal    
DOI: 10.1111/j.1540-8159.2010.02826.x     Document Type: Article

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