Familial hemophagocytic lymphohistiocytosis in a pediatric patient diagnosed by brain magnetic resonance imaging

Neuropediatrics

Volumn 42, Issue 5, 2011, Pages 191-193

  Van Egmond, M E ^a,b   Vermeulen, R J ^a   Peeters Scholte, C M P C D ^a,c   Augoustides Savvopoulou, P ^d   Abbink, F ^a   Boelens, J J ^e   Van Der Knaap, M S ^a  

^a VU UNIVERSITY MEDICAL CENTER   (Netherlands)

^b UNIVERSITY MEDICAL CENTER GRONINGEN   (Netherlands)

^c LEIDEN UNIVERSITY MEDICAL CENTER   (Netherlands)

^d ARISTOTLE UNIVERSITY OF THESSALONIKI   (Greece)

^e UNIVERSITY MEDICAL CENTER UTRECHT   (Netherlands)

Author keywords

allogeneic stem cell transplantation; familial hemophagocytic lymphohistiocytosis; magnetic resonance imaging; perivascular enhancement

Indexed keywords

ACICLOVIR; CEFTRIAXONE; CYCLOSPORIN; DEXAMETHASONE; DNA; ETOPOSIDE; GADOLINIUM; GLYCINE; LYSINE; MANNITOL; METHOTREXATE; METHYLPREDNISOLONE; PERFORIN; PREDNISOLONE; SERINE;

ACUTE DISSEMINATING ENCEPHALOMYELITIS; ALLOTRANSPLANTATION; ANTIVIRAL THERAPY; ARTICLE; BRAIN CORTEX; CASE REPORT; CHEMOTHERAPY; CLINICAL PROTOCOL; CORD BLOOD STEM CELL TRANSPLANTATION; DECUBITUS; DENTATE NUCLEUS; DEVELOPMENTAL DISORDER; DNA DETERMINATION; DRUG DOSE REDUCTION; ELECTROENCEPHALOGRAPHY; ENCEPHALOMYELITIS; EXON; FAMILY HISTORY; FOLLOW UP; GASTROINTESTINAL HEMORRHAGE; GENE MUTATION; HEMISPHERE; HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS; HETEROZYGOTE; HUMAN; IMAGE ENHANCEMENT; IMMUNOTHERAPY; INFANT; MALE; MENINGOENCEPHALITIS; NUCLEAR MAGNETIC RESONANCE IMAGING; PRIORITY JOURNAL; SEPTIC SHOCK; SHOCK; SPLENOMEGALY; STEROID THERAPY; THROMBOCYTE TRANSFUSION; TREATMENT RESPONSE; WHITE MATTER;

ANTI-INFLAMMATORY AGENTS; CEREBELLAR CORTEX; CEREBRAL CORTEX; DRUG THERAPY, COMBINATION; HETEROZYGOTE; HUMANS; IMMUNOSUPPRESSIVE AGENTS; INFANT; LYMPHOHISTIOCYTOSIS, HEMOPHAGOCYTIC; MAGNETIC RESONANCE IMAGING; MALE; MUTATION; PORE FORMING CYTOTOXIC PROTEINS;

EID: 81855226699     PISSN: 0174304X     EISSN: 14391899     Source Type: Journal    
DOI: 10.1055/s-0031-1287788     Document Type: Article

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