Bowel obstruction in patients with Alpers-Huttenlocher syndrome

Neuropediatrics

Volumn 42, Issue 5, 2011, Pages 194-196

  Spiegler, J ^a   Stefanova, I ^a   Hellenbroich, Y ^a   Sperner, J ^b  

^a Institut für Humangenetik   (Germany)

^b Schwerpunktpraxis Neuropädiatrie   (Germany)

Author keywords

Alpers Huttenlocher syndrome (AHS); constipation; EEG; gastrointestinal dysmotility; ketogenic diet; lacosamide; MRI; refractory convulsive status; urinary retention

Indexed keywords

ANALGESIC AGENT; DNA DIRECTED DNA POLYMERASE GAMMA; DOMPERIDONE; ERYTHROMYCIN; HARKOSERIDE; MACROGOL; METOCLOPRAMIDE; TOPIRAMATE;

ALPERS DISEASE; ARTICLE; ATAXIA; CASE REPORT; CHILD; CHILD DEATH; CONVULSION; DEVELOPMENTAL DISORDER; DISEASE SEVERITY; EPILEPTIC STATE; FEMALE; FLUID THERAPY; GASTROINTESTINAL MOTILITY DISORDER; HUMAN; INTESTINE OBSTRUCTION; INTESTINE TRANSIT TIME; KETOGENIC DIET; LIVER DYSFUNCTION; MALE; MASSAGE; MYOCLONUS EPILEPSY; PRESCHOOL CHILD; PRIORITY JOURNAL;

CHILD, PRESCHOOL; DIFFUSE CEREBRAL SCLEROSIS OF SCHILDER; DNA-DIRECTED DNA POLYMERASE; ELECTROENCEPHALOGRAPHY; FEMALE; HUMANS; INFANT; INTESTINAL OBSTRUCTION; MAGNETIC RESONANCE IMAGING; MALE;

EID: 81855172277     PISSN: 0174304X     EISSN: 14391899     Source Type: Journal    
DOI: 10.1055/s-0031-1287812     Document Type: Article

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