Management of inherited von Willebrand Disease in Italy: Results from the retrospective study on 1234 patients

Seminars in Thrombosis and Hemostasis

Volumn 37, Issue 5, 2011, Pages 511-521

  Federici, Augusto B ^a,b   Bucciarelli, Paolo ^b   Castaman, Giancarlo ^c   Baronciani, Luciano ^b   Canciani, Maria T ^b   Mazzucconi, Maria G ^d   Morfini, Massimo ^e   Rocino, Angiola ^f   Schiavoni, Mario ^g   Oliovecchio, Emily ^h   Iorio, Alfonso ^h   Mannucci, Pier M ^b  

^a UNIVERSITY OF MILAN   (Italy)

^b FONDAZIONE IRCCS CA GRANDA OSPEDALE MAGGIORE POLICLINICO   (Italy)

^c SAN BORTOLO HOSPITAL   (Italy)

^d SAPIENZA UNIVERSITY OF ROME   (Italy)

^e CAREGGI UNIVERSITY HOSPITAL   (Italy)

^f Pellegrini Hospital   (Italy)

^g POLICLINICO   (Italy)

^h UNIVERSITY OF PERUGIA   (Italy)

Author keywords

clinical; desmopressin; laboratory and molecular markers; mucosal bleeding; von Willebrand disease; von Willebrand factor assays; VWF FVIII concentrates

Indexed keywords

BLOOD CLOTTING FACTOR 8; BLOOD CLOTTING FACTOR 8 CONCENTRATE; DESMOPRESSIN; RECOMBINANT BLOOD CLOTTING FACTOR 8; VON WILLEBRAND FACTOR;

ADOLESCENT; ADULT; AGED; ARTICLE; BRAIN HEMORRHAGE; CHILD; CONTROLLED STUDY; DISEASE REGISTRY; EPISTAXIS; FAMILY HISTORY; FEMALE; GASTROINTESTINAL HEMORRHAGE; GENE MUTATION; GINGIVA BLEEDING; HEMARTHROSIS; HEMATOMA; HEMATURIA; HUMAN; ITALY; MAJOR CLINICAL STUDY; MALE; MEDICAL HISTORY; MENORRHAGIA; MOLECULAR DIAGNOSIS; MUCOSAL BLEEDING; POSTOPERATIVE HEMORRHAGE; PRESCHOOL CHILD; PRIORITY JOURNAL; RETROSPECTIVE STUDY; SCHOOL CHILD; VON WILLEBRAND DISEASE; WOUND HEMORRHAGE;

ADOLESCENT; ADULT; AGED; AGED, 80 AND OVER; CHILD; CHILD, PRESCHOOL; DEAMINO ARGININE VASOPRESSIN; FACTOR VIII; FEMALE; GENE FREQUENCY; HEMOSTATICS; HUMANS; INFANT; ITALY; MALE; MIDDLE AGED; MUTATION; RETROSPECTIVE STUDIES; VON WILLEBRAND DISEASES; VON WILLEBRAND FACTOR; YOUNG ADULT;

EID: 81755176084     PISSN: 00946176     EISSN: 10989064     Source Type: Journal    
DOI: 10.1055/s-0031-1281037     Document Type: Article

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