Right ventricular involvement in patients with fabrys disease and the effect of enzyme replacement therapy

RoFo Fortschritte auf dem Gebiet der Rontgenstrahlen und der Bildgebenden Verfahren

Volumn 183, Issue 11, 2011, Pages 1037-1042

  Wuest, W ^a   MacHann, W ^b   Breunig, F ^b   Weidemann, F ^b   Koestler, H ^b   Hahn, D ^b   Wanner, C ^b   Beer, M ^b  

^a UNIVERSITY HOSPITAL ERLANGEN   (Germany)

^b UNIVERSITY HOSPITAL WÜRZBURG   (Germany)

Author keywords

cardiac; metabolic Disorders; MR imaging

Indexed keywords

ARTICLE; CARDIAC IMAGING; CARDIOMYOPATHY; CLINICAL ARTICLE; ENZYME REPLACEMENT; FABRY DISEASE; HEART RIGHT VENTRICLE; HEART RIGHT VENTRICLE FUNCTION; HEART RIGHT VENTRICLE VOLUME; HEMODYNAMIC PARAMETERS; HUMAN; NUCLEAR MAGNETIC RESONANCE IMAGING; NUCLEAR MAGNETIC RESONANCE SCANNER; PRIORITY JOURNAL; PROSPECTIVE STUDY; TREATMENT OUTCOME;

ADULT; ALPHA-GALACTOSIDASE; CARDIOMYOPATHIES; DIASTOLE; ECHOCARDIOGRAPHY; FABRY DISEASE; FEMALE; FOLLOW-UP STUDIES; HUMANS; HYPERTROPHY, RIGHT VENTRICULAR; IMAGE PROCESSING, COMPUTER-ASSISTED; IMAGING, THREE-DIMENSIONAL; ISOENZYMES; MAGNETIC RESONANCE IMAGING, CINE; MALE; MIDDLE AGED; STROKE VOLUME; SYSTOLE; VENTRICULAR DYSFUNCTION, RIGHT;

EID: 80055081669     PISSN: 14389029     EISSN: 14389010     Source Type: Journal    
DOI: 10.1055/s-0031-1281744     Document Type: Article

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