Cutaneous granulomas in ataxia telangiectasia and other primary immunodeficiencies: Reflection of inappropriate immune regulation?

Dermatology

Volumn 223, Issue 1, 2011, Pages 13-19

  Chiam, L Y T ^a   Verhagen, M M M ^a   Haraldsson, A ^d   Wulffraat, N ^b   Driessen, G J ^c   Netea, M G ^a   Weemaes, C M R ^a   Seyger, M M B ^a   Van Deuren, M ^a  

^a RADBOUD UNIVERSITY MEDICAL CENTER   (Netherlands)

^b UNIVERSITY MEDICAL CENTER UTRECHT   (Netherlands)

^c SOPHIA CHILDREN S HOSPITAL   (Netherlands)

^d LANDSPITALI UNIVERSITY HOSPITAL   (Iceland)

Author keywords

Ataxia telangiectasia; B cells; Cutaneous granulomas; Immunodeficiency; Natural killer cells; T cells

Indexed keywords

ALPHA FETOPROTEIN; ANTIBIOTIC AGENT; CD19 ANTIGEN; CD3 ANTIGEN; CORTICOSTEROID; IMMUNOGLOBULIN; IMMUNOGLOBULIN A; IMMUNOGLOBULIN G; IMMUNOGLOBULIN M; T LYMPHOCYTE RECEPTOR; TACROLIMUS; TUBERCULOSTATIC AGENT;

ANTIBIOTIC THERAPY; ATAXIA TELANGIECTASIA; B LYMPHOCYTE; CASE REPORT; CD4+ T LYMPHOCYTE; CD8+ T LYMPHOCYTE; CHEST INFECTION; CHILD; CLINICAL EXAMINATION; CORTICOSTEROID THERAPY; DISEASE ASSOCIATION; ERYTHEMA; FAMILY HISTORY; FEMALE; GAMMA DELTA T LYMPHOCYTE; GENE MUTATION; HISTIOCYTE; HUMAN; IMMUNE DEFICIENCY; IMMUNOGLOBULIN A DEFICIENCY; IMMUNOGLOBULIN BLOOD LEVEL; IMMUNOGLOBULIN G DEFICIENCY; IMMUNOREGULATION; INTERSTITIAL LUNG DISEASE; MACROPHAGE; MALE; MEDICAL LITERATURE; NATURAL KILLER CELL; PATHOGENESIS; PRESCHOOL CHILD; PRIORITY JOURNAL; RECURRENT INFECTION; RESPIRATORY FAILURE; REVIEW; SKIN BIOPSY; SKIN GRANULOMA; SKIN ULCER; UPPER RESPIRATORY TRACT INFECTION;

ATAXIA TELANGIECTASIA; B-LYMPHOCYTES; CHILD; CHILD, PRESCHOOL; FEMALE; GRANULOMA; HUMANS; IMMUNOGLOBULIN A; IMMUNOGLOBULIN G; IMMUNOLOGIC DEFICIENCY SYNDROMES; INFANT; LEG DERMATOSES; MALE; SKIN DISEASES; T-LYMPHOCYTES;

EID: 80053977318     PISSN: 10188665     EISSN: 14219832     Source Type: Journal    
DOI: 10.1159/000330335     Document Type: Review

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