Otologic and audiologic manifestations of Hutchinson-Gilford progeria syndrome

Laryngoscope

Volumn 121, Issue 10, 2011, Pages 2250-2255

  Guardiani, Elizabeth ^a   Zalewski, Christopher ^b   Brewer, Carmen ^b   Merideth, Melissa ^c   Introne, Wendy ^c   Smith, Ann C M ^c   Gordon, Leslie ^d,e   Gahl, William ^c   Kim, H Jeffrey ^a,b  

^a GEORGETOWN UNIVERSITY HOSPITAL   (United States)

^b NATIONAL INSTITUTE ON DEAFNESS AND OTHER COMMUNICATION DISORDERS   (United States)

^c NATIONAL HUMAN GENOME RESEARCH INSTITUTE   (United States)

^d BROWN UNIVERSITY   (United States)

^e BOSTON CHILDREN S HOSPITAL   (United States)

Author keywords

external ear; hearing loss; Hutchinson Gilford Progeria syndrome; middle ear; progeria

Indexed keywords

ADOLESCENT; ARTICLE; CERUMEN IMPACTION; CHILD; CLINICAL ARTICLE; CONTROLLED STUDY; EAR CARTILAGE; EXTERNAL AUDITORY CANAL; FEMALE; GENE MUTATION; HEARING ACUITY; HEARING LOSS; HUMAN; HYPOPLASIA; MALE; OTITIS MEDIA; OTOACOUSTIC EMISSION; OTORHINOLARYNGOLOGY; PHENOTYPE; PRIORITY JOURNAL; PROGERIA; PROSPECTIVE STUDY;

ACOUSTIC IMPEDANCE TESTS; AUDIOMETRY, PURE-TONE; CHILD; CHILD, PRESCHOOL; COHORT STUDIES; FEMALE; FOLLOW-UP STUDIES; HEARING LOSS, CONDUCTIVE; HUMANS; INCIDENCE; INFANT; MALE; MONITORING, PHYSIOLOGIC; OTOACOUSTIC EMISSIONS, SPONTANEOUS; PROGERIA; PROSPECTIVE STUDIES; RISK ASSESSMENT;

EID: 80053210800     PISSN: 0023852X     EISSN: 15314995     Source Type: Journal    
DOI: 10.1002/lary.22151     Document Type: Article

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