Insights into Krabbe disease from structures of galactocerebrosidase

Proceedings of the National Academy of Sciences of the United States of America

Volumn 108, Issue 37, 2011, Pages 15169-15173

  Deane, Janet E ^a   Graham, Stephen C ^b   Kim, Nee Na ^c   Stein, Penelope E ^c   McNair, Rosamund ^c   Cachón González, M Begoña ^c   Cox, Timothy M ^c   Reada, Randy J ^a  

^a UNIVERSITY OF CAMBRIDGE   (United Kingdom)

^b UNIVERSITY OF CAMBRIDGE   (United Kingdom)

^c UNIVERSITY OF CAMBRIDGE   (United Kingdom)

Author keywords

Glycoside hydrolase family 59; Glycosy hydrolase

Indexed keywords

GALACTOSYLCERAMIDASE;

ARTICLE; CONTROLLED STUDY; CRYSTAL STRUCTURE; ENZYME BINDING; ENZYME STRUCTURE; GLOBOID CELL LEUKODYSTROPHY; HUMAN; HUMAN CELL; MUTATION; PRIORITY JOURNAL;

ANIMALS; BINDING SITES; CRYSTALLOGRAPHY, X-RAY; GALACTOSYLCERAMIDASE; GALACTOSYLCERAMIDES; HEK293 CELLS; HUMANS; LEUKODYSTROPHY, GLOBOID CELL; MICE; MODELS, MOLECULAR; MUTATION; PROTEIN STRUCTURE, SECONDARY; SUBSTRATE SPECIFICITY;

EID: 80053056049     PISSN: 00278424     EISSN: 10916490     Source Type: Journal    
DOI: 10.1073/pnas.1105639108     Document Type: Article

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