Portopulmonary hypertension secondary to congenital extrahepatic portosystemic shunt with heterotaxy and polysplenia: A cause of sudden death in an infant

Pediatric Pulmonology

Volumn 46, Issue 10, 2011, Pages 1041-1044

  Kobayashi, Daisuke ^a   Edwards, Henry D ^b   Singh, Jasmeet ^b   Nadkarni, Milan D ^b   Lantz, Patrick E ^b   Cook, Amanda L ^a  

^a WAYNE STATE UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b WAKE FOREST SCHOOL OF MEDICINE   (United States)

Author keywords

heterotaxy; interrupted inferior vena cava; polysplenia; portopulmonary hypertension; portosystemic shunt; sudden death

Indexed keywords

ACCESSORY SPLEEN; APNEA; ASCITES; AUTOPSY; BRADYCARDIA; BRONCHIOLITIS; CARDIOMEGALY; CASE REPORT; CHILD; COMPUTER ASSISTED TOMOGRAPHY; CONGENITAL PORTOSYSTEMIC SHUNT; ECHOGRAPHY; FEMALE; HEMOPERITONEUM; HETEROTAXY SYNDROME; HUMAN; INFANT; PARACENTESIS; PORTOPULMONARY HYPERTENSION; PRIORITY JOURNAL; RADIOGRAPHY; RESPIRATORY DISTRESS; RESUSCITATION; RETROSPECTIVE STUDY; REVIEW; SHOCK; SUDDEN DEATH; THORAX RADIOGRAPHY; THROMBOCYTOPENIC PURPURA; VOMITING;

DEATH, SUDDEN; FATAL OUTCOME; FEMALE; HETEROTAXY SYNDROME; HUMANS; HYPERTENSION, PULMONARY; INFANT; PORTAL SYSTEM; PORTAL VEIN;

EID: 80052968923     PISSN: 87556863     EISSN: 10990496     Source Type: Journal    
DOI: 10.1002/ppul.21463     Document Type: Review

References (5)

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