Left ventricular noncompaction syndrome masquerading or misdiagnosed as congenital long QT syndrome: Remember QT prolongation does not equal long QT syndrome

Congenital Heart Disease

Volumn 6, Issue 5, 2011, Pages 492-498

  Coleman, Mira A ^a   Bos, J Martijn ^b   Phillips, Sabrina D ^c   Souza, Joseph J ^d   Ackerman, Michael J ^b,c  

^a MAYO CLINIC COLLEGE OF MEDICINE   (United States)

^b MAYO GRADUATE SCHOOL   (United States)

^c MAYO CLINIC   (United States)

^d Ashville Cardiology Associates   (United States)

Author keywords

Arrhythmias; Left ventricular noncompaction; Long QT syndrome; LQTS; LVNC; QT prolongation

Indexed keywords

ALPHA TROPOMYOSIN; DYSTROBREVIN; POTASSIUM CHANNEL KCNQ1; SODIUM CHANNEL NAV1.5;

ACTC GENE; ADULT; ANAMNESIS; ARTICLE; CASE REPORT; COMPUTER ASSISTED TOMOGRAPHY; CONGENITAL HEART DISEASE; CONGESTIVE CARDIOMYOPATHY; DES GENE; DIAGNOSTIC ERROR; ECHOCARDIOGRAPHY; ELECTROCARDIOGRAPHY; FEMALE; GENE; GENETIC SCREENING; HEART DENERVATION; HEART LEFT BUNDLE BRANCH BLOCK; HEART LEFT VENTRICLE EJECTION FRACTION; HEART MUSCLE; HEART VENTRICLE FIBRILLATION; HUMAN; KCNH2 GENE; LDB3 GENE; LONG QT SYNDROME; MUTATIONAL ANALYSIS; MYBPC3 GENE; MYH7 GENE; PRIORITY JOURNAL; QT PROLONGATION; QUALITY OF LIFE; SECOND DEGREE ATRIOVENTRICULAR BLOCK; SINUS RHYTHM; TAZ GENE; TNNI3 GENE; VENTRICULAR NONCOMPACTION;

ADULT; ANTI-ARRHYTHMIA AGENTS; CARDIAC PACING, ARTIFICIAL; DEFIBRILLATORS, IMPLANTABLE; DIAGNOSTIC ERRORS; ELECTRIC COUNTERSHOCK; ELECTROCARDIOGRAPHY; FEMALE; HUMANS; ISOLATED NONCOMPACTION OF THE VENTRICULAR MYOCARDIUM; LONG QT SYNDROME; PREDICTIVE VALUE OF TESTS; TOMOGRAPHY, X-RAY COMPUTED; TREATMENT OUTCOME; VENTRICULAR FIBRILLATION;

EID: 80052865395     PISSN: 1747079X     EISSN: 17470803     Source Type: Journal    
DOI: 10.1111/j.1747-0803.2011.00531.x     Document Type: Article

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