Absence of a gender gap in survival. An analysis of the Italian registry for cystic fibrosis in the paediatric age

Journal of Cystic Fibrosis

Volumn 10, Issue 5, 2011, Pages 313-317

  Viviani, Laura ^a   Bossi, Anna ^a   Assael, Baroukh Maurice ^b  

^a UNIVERSITY OF MILAN   (Italy)

^b Center for Cystic Fibrosis   (Italy)

Author keywords

[No Author keywords available]

Indexed keywords

ADOLESCENT; ARTICLE; CHILD; CHILDHOOD DISEASE; CYSTIC FIBROSIS; FEMALE; FOLLOW UP; GENE DELETION; GENE MUTATION; GENOTYPE; HAZARD RATIO; HUMAN; INFANT; ITALY; MAJOR CLINICAL STUDY; MALE; MECONIUM ILEUS; MORBIDITY; MORTALITY; NEWBORN; PRESCHOOL CHILD; SCHOOL CHILD; SEX DIFFERENCE; SEX RATIO; SURVIVAL RATE;

ADOLESCENT; AGE DISTRIBUTION; CHILD; CHILD, PRESCHOOL; CYSTIC FIBROSIS; FEMALE; HUMANS; INCIDENCE; INFANT; ITALY; KAPLAN-MEIER ESTIMATE; LONGITUDINAL STUDIES; MALE; REGISTRIES; RISK FACTORS; SEX DISTRIBUTION;

EID: 80052465621     PISSN: 15691993     EISSN: 18735010     Source Type: Journal    
DOI: 10.1016/j.jcf.2011.03.007     Document Type: Article

References (20)

1. Davis P.B. Cystic fibrosis since 1938. Am J Respir Crit Care Med 2006, 173:475-482.
2. Corey M., Farewell V. Determinants of mortality from cystic fibrosis in Canada, 1970-1989. Am J Epidemiol 1996, 143:1007-1017.
3. Rosenfeld M., Davis R., FitzSimmons S., Pepe M., Ramsey B. Gender gap in cystic fibrosis mortality. Am J Epidemiol 1997, 145:794-803.
4. Kulich M., Rosenfeld M., Goss C.H., Wilmott R. Improved survival among young patients with cystic fibrosis. J Pediatr 2003, 142:631-636.
5. Assael B.M., Castellani C., Ocampo M.B., Iansa P., Callegaro A., Valsecchi M.G. Epidemiology and survival analysis of cystic fibrosis in an area of intense neonatal screening over 30years. Am J Epidemiol 2002, 156:397-401.
6. Verma N., Bush A., Buchdal R. Is there still a gender gap in cystic fibrosis?. Chest 2005, 128:2824-2834.
7. Viviani L., Padoan R., Giglio L., Bossi A. The Italian registry for cystic fibrosis: what has changed in the last decade. Epidemiol Prev 2003, 27:91-96.
8. Bossi A., Casazza G., Padoan R., Milani S. Assemblea Dei Direttori Dei Centri. What is the incidence of cystic fibrosis in Italy? Data from the National Registry (1988-2001). Hum Biol 2004, 76:455-467.
9. Rosenstein B.J., Cutting G.R. The diagnosis of cystic fibrosis: a consensus statement. Cystic Fibrosis Foundation Consensus Panel. J Pediatr 1998, 132:589-595.
10. Annuario Statististico Italiano. Istituto Centrale di Statistica. Editions from 1988 to 2004.
11. Dodge J.A., Lewis P.A., Stanton M., Wilsher J. Cystic fibrosis mortality and survival in the UK: 1947-2003. Eur Respir J 2007, 29:522-526.
12. Bobadilla J.L., Macek M., Fine J.P., Farrell P.M. Cystic fibrosis: a worldwide analysis of CFTR mutations-correlation with incidence data and application to screening. Hum Mutat 2002, 19:575-606.
13. Rendine S., Calafell F., Cappello N., et al. Genetic history of cystic fibrosis mutations in Italy. I. Regional distribution. Ann Hum Genet 1997, 61:411-424.
14. Moran A., Doherty L., Wang X., Thomas W. Abnormal glucose metabolism in cystic fibrosis. J Pediatr 1998, 133:10-17.
15. Maselli J.H., Sontag M.K., Norris J.M., MacKenzie T., Wagener J.S., Accurso F.J. Risk factors for initial acquisition of Pseudomonas aeruginosa in children with cystic fibrosis identified by newborn screening. Pediatr Pulmonol 2003, 35:257-262.
16. Demko C.A., Byard P.J., Davis P.B. Gender differences in cystic fibrosis: Pseudomonas aeruginosa infection. J Clin Epidemiol 1995, 48:1041-1049.
17. Sims E.J., Green M.W., Mehta A. Decreased lung function in female but not male subjects with established cystic fibrosis-related diabetes. Diab Care 2005, 28:1581-1587.
18. Lai H.C., Kosorok M.R., Laxova A., Makholm L.M., Farrell P.M. Delayed diagnosis of US females with cystic fibrosis. Am J Epidemiol 2002, 156:165-173.
19. Coakley R.D., Sun H., Clunes L.A., Rasmussen J.E., Stackhouse J.R., Okada S.F., et al. 17beta-Estradiol inhibits Ca2+-dependent homeostasis of airway surface liquid volume in human cystic fibrosis airway epithelia. J Clin Invest 2008, 118:4025-4035.
20. Zeitlin P.L. Cystic fibrosis and estrogens: a perfect storm. J Clin Invest 2008, 118:3841-3844.