Modeling human trinucleotide repeat diseases in drosophila

International Review of Neurobiology

Volumn 99, Issue , 2011, Pages 191-212

  Yu, Zhenming ^a   Bonini, Nancy M ^a,b  

^a UNIVERSITY OF PENNSYLVANIA   (United States)

^b HOWARD HUGHES MEDICAL INSTITUTE   (United States)

Author keywords

Antisense transcription; Chaperons; Drosophila models; Noncoding repeat RNA toxicity diseases; Polyglutamine diseases; Trinucleotide repeat diseases; Trinucleotide repeat instability; Ubiqutin proteasome system

Indexed keywords

ATAXIN 2; ATAXIN 3; BINDING PROTEIN; CHAPERONE; POLYGLUTAMINE; RNA; STEM CELL ANTIGEN 1; UNCLASSIFIED DRUG;

5' UNTRANSLATED REGION; ANDROGEN RECEPTOR GENE; BINDING AFFINITY; BINDING SITE; BOOK; CAG REPEAT; DEGENERATIVE DISEASE; DISEASE ACTIVITY; DISEASE ASSOCIATION; DROSOPHILA; FRAGILE X MENTAL RETARDATION 1 GENE; FRAGILE X SYNDROME GENE; GENE; GENE EXPRESSION; GENE FUNCTION; GENE INTERACTION; GENETIC ASSOCIATION; GENETIC DISORDER; GENETIC TRANSCRIPTION; GENOME ANALYSIS; HUMAN; HUNTINGTON CHOREA; MOLECULAR DYNAMICS; MOLECULAR PATHOLOGY; NONHUMAN; POLYGLUTAMINE DISEASE; PRIORITY JOURNAL; PROMOTER REGION; PROTEIN DEFECT; PROTEIN DEGRADATION; PROTEIN DOMAIN; PROTEIN FOLDING; PROTEIN FUNCTION; PROTEIN PHOSPHORYLATION; PROTEIN PROTEIN INTERACTION; PROTEIN RNA BINDING; SEQUENCE ANALYSIS; SPINAL MUSCULAR ATROPHY; SPINOCEREBELLAR DEGENERATION; TRINUCLEOTIDE REPEAT;

EID: 80052451891     PISSN: 00747742     EISSN: None     Source Type: Book Series    
DOI: 10.1016/B978-0-12-387003-2.00008-2     Document Type: Chapter

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