Management of sickle cell disease: Out-patient and community aspects

Paediatrics and Child Health

Volumn 21, Issue 8, 2011, Pages 357-362

  Telfer, Paul T ^a  

^a ROYAL LONDON HOSPITAL   (United Kingdom)

Author keywords

Community care; Neonatal screening; Pneumococcal disease; Primary care; Sickle cell disease; Specialist centre; Stroke

Indexed keywords

DEFERASIROX; DEFERIPRONE; DEFEROXAMINE; HEMOGLOBIN; HEMOGLOBIN F; HYDROXYUREA; PENICILLIN G; PNEUMOCOCCUS VACCINE;

ACADEMIC ACHIEVEMENT; ACUTE CHEST SYNDROME; ALLOGENIC BONE MARROW TRANSPLANTATION; ANTIBIOTIC PROPHYLAXIS; BETA THALASSEMIA; BRAIN INFARCTION; COMMUNITY CARE; DNA DETERMINATION; EXCHANGE BLOOD TRANSFUSION; GENOTYPE; HEMOGLOBIN ANALYSIS; HETEROZYGOTE; HIGH PERFORMANCE LIQUID CHROMATOGRAPHY; HUMAN; INFECTION PREVENTION; INVASIVE PNEUMOCOCCAL DISEASE; IRON CHELATION; IRON OVERLOAD; ISOELECTRIC FOCUSING; LONG TERM CARE; MORBIDITY; MORTALITY; NEWBORN SCREENING; OUTPATIENT CARE; PAIN; PHLEBOTOMY; PNEUMOCOCCAL INFECTION; QUALITY OF LIFE; REVIEW; SELF ESTEEM; SICKLE CELL ANEMIA; STROKE;

EID: 80051686015     PISSN: 17517222     EISSN: 1878206X     Source Type: Journal    
DOI: 10.1016/j.paed.2011.03.005     Document Type: Review

References (14)

1. Streetly A., Latinovic R., Henthorn J. Positive screening and carrier results for the England-wide universal newborn sickle cell screening programme by ethnicity and area for 2005-07. J Clin Pathol Jul 2010, 63:626-629.
2. Streetly A., Latinovic R., Hall K., Henthorn J. Implementation of universal newborn bloodspot screening for sickle cell disease and other clinically significant haemoglobinopathies in England: screening results for 2005-7. J Clin Pathol 2009 Jan, 62:26-30.
3. Gill F.M., Sleeper L.A., Weiner S.J., et al. Clinical events in the first decade in a cohort of infants with sickle cell disease. Cooperative study of Sickle Cell Disease. Blood 1995 Jul 15, 86:776-783.
4. Lee A., Thomas P., Cupidore L., Serjeant B., Serjeant G. Improved survival in homozygous sickle cell disease: lessons from a cohort study. BMJ 1995 Dec 16, 311:1600-1602.
5. Telfer P., Coen P., Chakravorty S., et al. Clinical outcomes in children with sickle cell disease living in England: a neonatal cohort in East London. Haematologica 2007 Jul, 92:905-912.
6. Quinn C.T., Rogers Z.R., Buchanan G.R. Survival of children with sickle cell disease. Blood 2004 Jun 1, 103:4023-4027.
7. Charache S., Terrin M.L., Moore R.D., et al. Effect of hydroxyurea on the frequency of painful crises in sickle cell anemia. Investigators of the multicenter study of hydroxyurea in Sickle Cell Anemia. N Engl J Med 1995 May 18, 332:1317-1322.
8. Hankins J.S., Ware R.E., Rogers Z.R., et al. Long-term hydroxyurea therapy for infants with sickle cell anemia: the HUSOFT extension study. Blood 2005 Oct 1, 106:2269-2275.
9. Ware R.E. How I use hydroxyurea to treat young patients with sickle cell anemia. Blood Jul 1 2010, 115:5300-5311.
10. Vichinsky E., Onyekwere O., Porter J., et al. A randomised comparison of deferasirox versus deferoxamine for the treatment of transfusional iron overload in sickle cell disease. Br J Haematol 2007 Feb, 136:501-508.
11. Adams R.J., McKie V.C., Hsu L., et al. Prevention of a first stroke by transfusions in children with sickle cell anemia and abnormal results on transcranial Doppler ultrasonography. N Engl J Med 1998 Jul 2, 339:5-11.
12. Vichinsky E.P., Luban N.L., Wright E., et al. Prospective RBC phenotype matching in a stroke-prevention trial in sickle cell anemia: a multicenter transfusion trial. Transfusion 2001 Sep, 41:1086-1092.
13. NHS screening programmes: Sickle Cell and Thalassaemia. Handbook for laboratories September 2009, Accessed at: http://sct.screening.nhs.uk.
14. NHS screening programmes: sickle cell and thalassaemia. Sickle cell disease in childhood. Standards and guidelines for clinical care October 2010, Accessed at: http://sct.screening.nhs.uk. 2nd Edn.