-
2
-
-
33646091498
-
Hypertonic saline for cystic fibrosis
-
Aziz I. Kastelik J.A. (2006) Hypertonic saline for cystic fibrosis. N Engl J Med 354: 1848–1850.
-
(2006)
N Engl J Med
, vol.354
, pp. 1848-1850
-
-
Aziz, I.1
Kastelik, J.A.2
-
3
-
-
34848870898
-
Anti-inflammatory approaches to cystic fibrosis airways disease
-
Balfour-Lynn I.M. (2007) Anti-inflammatory approaches to cystic fibrosis airways disease. Curr Opin Pulm Med 13: 522–528.
-
(2007)
Curr Opin Pulm Med
, vol.13
, pp. 522-528
-
-
Balfour-Lynn, I.M.1
-
4
-
-
78649483621
-
Phase III study of inhaled dry powder mannitol (Bronchitol™) in cystic fibrosis ’ results from the 6 month open label phase
-
[abstract]
-
Bilton D. Robinson P. Cooper P. Gallagher C. Kolbe J. Charlton B. (2010) Phase III study of inhaled dry powder mannitol (Bronchitol™) in cystic fibrosis ’ results from the 6 month open label phase. Am J Respir Crit Care Med 181: A2338–A2338. [abstract].
-
(2010)
Am J Respir Crit Care Med
, vol.181
, pp. A2338-A2338
-
-
Bilton, D.1
Robinson, P.2
Cooper, P.3
Gallagher, C.4
Kolbe, J.5
Charlton, B.6
-
5
-
-
33746081253
-
Causes of chronic diarrhea
-
Binder H.J. (2006) Causes of chronic diarrhea. N Engl J Med 355: 236–239.
-
(2006)
N Engl J Med
, vol.355
, pp. 236-239
-
-
Binder, H.J.1
-
7
-
-
77950787429
-
Inhaled mannitol improves the hydration and surface properties of sputum in patients with cystic fibrosis
-
Daviskas E. Anderson S.D. Jaques A. Charlton B. (2010) Inhaled mannitol improves the hydration and surface properties of sputum in patients with cystic fibrosis. Chest 137: 861–868.
-
(2010)
Chest
, vol.137
, pp. 861-868
-
-
Daviskas, E.1
Anderson, S.D.2
Jaques, A.3
Charlton, B.4
-
8
-
-
50849135221
-
Hydrator therapies for cystic fibrosis in lung disease
-
Donaldson S.H. (2008) Hydrator therapies for cystic fibrosis in lung disease. Ped Pulm 43: S18's23.
-
(2008)
Ped Pulm
, vol.43
, pp. S18-S23
-
-
Donaldson, S.H.1
-
12
-
-
50849121444
-
The science of aerosol delivery in cystic fibrosis
-
Geller D.E. (2008) The science of aerosol delivery in cystic fibrosis. Ped Pulm 43: S5's17.
-
(2008)
Ped Pulm
, vol.43
, pp. S5-S17
-
-
Geller, D.E.1
-
13
-
-
0036304163
-
Pharmacokinetics and bioavailability of aerosolized tobramycin in cystic fibrosis
-
Geller D.E. Pitlick W.H. Nardella P.A. Tracewell W.G. Ramsey B.W. (2002) Pharmacokinetics and bioavailability of aerosolized tobramycin in cystic fibrosis. Chest 122: 219–226.
-
(2002)
Chest
, vol.122
, pp. 219-226
-
-
Geller, D.E.1
Pitlick, W.H.2
Nardella, P.A.3
Tracewell, W.G.4
Ramsey, B.W.5
-
14
-
-
0142043977
-
State of the art: pathophysiology and management of pulmonary infections in cystic fibrosis
-
Gibson R.L. Burns J.L. Ramsey B.W. (2003) State of the art: pathophysiology and management of pulmonary infections in cystic fibrosis. Am J Respir Crit Care Med 168: 918–951.
-
(2003)
Am J Respir Crit Care Med
, vol.168
, pp. 918-951
-
-
Gibson, R.L.1
Burns, J.L.2
Ramsey, B.W.3
-
15
-
-
0026831341
-
Mucoid pseudomonas aeruginosa is a marker of poor survival in cystic fibrosis
-
Henry R.L. Mellis C.M. Petrovic L. (1992) Mucoid pseudomonas aeruginosa is a marker of poor survival in cystic fibrosis. Ped Pulm 12: 158–161.
-
(1992)
Ped Pulm
, vol.12
, pp. 158-161
-
-
Henry, R.L.1
Mellis, C.M.2
Petrovic, L.3
-
16
-
-
0036736583
-
A randomized clinical trial of nebulized tobramycin or colistin in cystic fibrosis
-
Hodson M.E. Gallagher C.G. Govan J.R. (2002) A randomized clinical trial of nebulized tobramycin or colistin in cystic fibrosis. Eur Respir J 20: 658–664.
-
(2002)
Eur Respir J
, vol.20
, pp. 658-664
-
-
Hodson, M.E.1
Gallagher, C.G.2
Govan, J.R.3
-
17
-
-
0028920643
-
Cystic fibrosis epithelial cells have a receptor for pathogenic bacteria on their apical surface
-
Immundo L. Barasch J. Prince A. Al-Awquit Q. (1995) Cystic fibrosis epithelial cells have a receptor for pathogenic bacteria on their apical surface. Proc Natl Acad Sci U S A 92: 3019–3023.
-
(1995)
Proc Natl Acad Sci U S A
, vol.92
, pp. 3019-3023
-
-
Immundo, L.1
Barasch, J.2
Prince, A.3
Al-Awquit, Q.4
-
18
-
-
44649166466
-
Inhaled mannitol improves lung function in cystic fibrosis
-
Jaques A. Daviskas E. Turton J.A. (2008) Inhaled mannitol improves lung function in cystic fibrosis. Chest 133: 1388–1396.
-
(2008)
Chest
, vol.133
, pp. 1388-1396
-
-
Jaques, A.1
Daviskas, E.2
Turton, J.A.3
-
19
-
-
0023265976
-
Colistin inhalation therapy in cystic fibrosis patients with chronic pseudomonas aeruginosa lung infection
-
Jensen T. Pedersen S.S. Garne S. Heilmann C. Hoiby N. Koch C. (1987) Colistin inhalation therapy in cystic fibrosis patients with chronic pseudomonas aeruginosa lung infection. J Antimicrob Chemother 19: 831–838.
-
(1987)
J Antimicrob Chemother
, vol.19
, pp. 831-838
-
-
Jensen, T.1
Pedersen, S.S.2
Garne, S.3
Heilmann, C.4
Hoiby, N.5
Koch, C.6
-
20
-
-
50149098401
-
Effectiveness of PTC124 treatment of cystic fibrosis caused by nonsense mutations: a prospective phase II trial
-
Kerem E. Hirawat S. Armoni S. Yaakov Y. Shoseyou D. Cohen M. (2008) Effectiveness of PTC124 treatment of cystic fibrosis caused by nonsense mutations: a prospective phase II trial. Lancet 372: 719–727.
-
(2008)
Lancet
, vol.372
, pp. 719-727
-
-
Kerem, E.1
Hirawat, S.2
Armoni, S.3
Yaakov, Y.4
Shoseyou, D.5
Cohen, M.6
-
21
-
-
0030845454
-
Rheology of cystic fibrosis sputum after in vitro treatment with hypertonic saline alone and in combination with recombinant human deoxyribonuclease
-
King M. Dasgupta B. Tomkiewcz R.P. Brown N. (1997) Rheology of cystic fibrosis sputum after in vitro treatment with hypertonic saline alone and in combination with recombinant human deoxyribonuclease. Am J Respir Crit Care Med 156: 173–177.
-
(1997)
Am J Respir Crit Care Med
, vol.156
, pp. 173-177
-
-
King, M.1
Dasgupta, B.2
Tomkiewcz, R.P.3
Brown, N.4
-
22
-
-
0031921423
-
Anti-inflammatory activity of macrolides: a new therapeutic potential?
-
Labro M.T. (1998) Anti-inflammatory activity of macrolides: a new therapeutic potential?. J Antimicrob Chemother 41: 37–46.
-
(1998)
J Antimicrob Chemother
, vol.41
, pp. 37-46
-
-
Labro, M.T.1
-
25
-
-
73449118258
-
Comparison of inhaled mannitol, daily rhDNase and a combination of both in children with cystic fibrosis: a randomized trial
-
Minasian C. Wallis C. Metcalfe C. Bush A. (2010) Comparison of inhaled mannitol, daily rhDNase and a combination of both in children with cystic fibrosis: a randomized trial. Thorax 65: 51–56.
-
(2010)
Thorax
, vol.65
, pp. 51-56
-
-
Minasian, C.1
Wallis, C.2
Metcalfe, C.3
Bush, A.4
-
26
-
-
79960112178
-
A multi-cycle open label study of nebulized liposomal amikacin (Arikace™) in the treatment of cystic fibrosis patients with chronic pseudomonas aeruginosa lung infection
-
Minic P. Fustic S. Solyom E. (2010) A multi-cycle open label study of nebulized liposomal amikacin (Arikace™) in the treatment of cystic fibrosis patients with chronic pseudomonas aeruginosa lung infection. Ped Pulm 45: S33's33.
-
(2010)
Ped Pulm
, vol.45
, pp. S33-S33
-
-
Minic, P.1
Fustic, S.2
Solyom, E.3
-
27
-
-
79960129524
-
Denufosol improved lung function and was well tolerated in adolescents with cystic fibrosis
-
Moss R.B. Schaberg A. Tian W. Xue X. Ramsey B. Accurso F.J. (2010) Denufosol improved lung function and was well tolerated in adolescents with cystic fibrosis. Ped Pulm 45: S33's33.
-
(2010)
Ped Pulm
, vol.45
, pp. S33-S33
-
-
Moss, R.B.1
Schaberg, A.2
Tian, W.3
Xue, X.4
Ramsey, B.5
Accurso, F.J.6
-
30
-
-
33750999611
-
Advances in cystic fibrosis therapies
-
Rowe S.M. Clancy J.P. (2006) Advances in cystic fibrosis therapies. Curr Opin Pediatr 18: 604–613.
-
(2006)
Curr Opin Pediatr
, vol.18
, pp. 604-613
-
-
Rowe, S.M.1
Clancy, J.P.2
-
31
-
-
18344387226
-
Mechanisms of disease: cystic fibrosis
-
Rowe S.M. Miller S. Sorscher E.J. (2005) Mechanisms of disease: cystic fibrosis. N Engl J Med 352: 1992–2001.
-
(2005)
N Engl J Med
, vol.352
, pp. 1992-2001
-
-
Rowe, S.M.1
Miller, S.2
Sorscher, E.J.3
-
32
-
-
77951887288
-
Effect of azithromycin on pulmonary function in patients with cystic fibrosis uninfected with Pseudomonas aeruginosa
-
Saiman L. Anstead M. Mayer-Hamblett N. Lands L.C. Kloster M. Hocevar-Trnka J. (2010) Effect of azithromycin on pulmonary function in patients with cystic fibrosis uninfected with Pseudomonas aeruginosa. JAMA 303: 1707–1715.
-
(2010)
JAMA
, vol.303
, pp. 1707-1715
-
-
Saiman, L.1
Anstead, M.2
Mayer-Hamblett, N.3
Lands, L.C.4
Kloster, M.5
Hocevar-Trnka, J.6
-
33
-
-
0141816759
-
The macrolide study group: a multicenter, randomized, placebo controlled, double-blind trial of azithromycin in patients with cystic fibrosis chronically infected with Pseudomonas aeruginosa
-
Saiman L. Marshall B.C. Mayer-Hamblett N. Burns J.L. Quittner A.L. Cibene D.A. (2003) The macrolide study group: a multicenter, randomized, placebo controlled, double-blind trial of azithromycin in patients with cystic fibrosis chronically infected with Pseudomonas aeruginosa. JAMA 290: 1749–1756.
-
(2003)
JAMA
, vol.290
, pp. 1749-1756
-
-
Saiman, L.1
Marshall, B.C.2
Mayer-Hamblett, N.3
Burns, J.L.4
Quittner, A.L.5
Cibene, D.A.6
-
34
-
-
0035922668
-
Comparison of hypertonic saline and alternate-day or daily recombinant deoxyribonuclease in children with cystic fibrosis: a randomized trial
-
Suri R. Metcalfe C. Lees B. Grieve R. Flather M. DPhil C.N. (2001) Comparison of hypertonic saline and alternate-day or daily recombinant deoxyribonuclease in children with cystic fibrosis: a randomized trial. Lancet 358: 1316–1321.
-
(2001)
Lancet
, vol.358
, pp. 1316-1321
-
-
Suri, R.1
Metcalfe, C.2
Lees, B.3
Grieve, R.4
Flather, M.5
DPhil, C.N.6
-
36
-
-
34447498842
-
Inhaled mannitol in cystic fibrosis
-
Wills P.J. (2007) Inhaled mannitol in cystic fibrosis. Expert Opin Investig Drugs 16: 1121–1126.
-
(2007)
Expert Opin Investig Drugs
, vol.16
, pp. 1121-1126
-
-
Wills, P.J.1
-
38
-
-
34250751848
-
Emerging drug treatments for cystic fibrosis
-
Zeitlin P.L. (2007) Emerging drug treatments for cystic fibrosis. Expert Opin Emerging Drugs 12: 329–336.
-
(2007)
Expert Opin Emerging Drugs
, vol.12
, pp. 329-336
-
-
Zeitlin, P.L.1
|