-
1
-
-
78651041685
-
Degenerative disease of the central nervous system in New Guinea: the endemic occurrence of "kuru" in the native population
-
Gajdusek DC, Zigas V. Degenerative disease of the central nervous system in New Guinea: the endemic occurrence of "kuru" in the native population. N Engl J Med 1957; 257: 974-8.
-
(1957)
N Engl J Med
, vol.257
, pp. 974-978
-
-
Gajdusek, D.C.1
Zigas, V.2
-
2
-
-
49749220574
-
Scrapie and kuru
-
Hadlow WJ. Scrapie and kuru. Lancet 1959; 2: 289-90.
-
(1959)
Lancet
, vol.2
, pp. 289-290
-
-
Hadlow, W.J.1
-
3
-
-
0014021742
-
Experimental transmission of a kuru-like syndrome to chimpanzees
-
Gajdusek DC, Gibbs CJ Jr, Alpers M. Experimental transmission of a kuru-like syndrome to chimpanzees. Nature 1966; 209: 794-6.
-
(1966)
Nature
, vol.209
, pp. 794-796
-
-
Gajdusek, D.C.1
Gibbs Jr, C.J.2
Alpers, M.3
-
4
-
-
0014430962
-
Creutzfeldt-Jakob disease (spongiform encephalopathy): transmission to the chimpanzee
-
Gibbs CJ Jr, Gajdusek DC, Asher DM et al. Creutzfeldt-Jakob disease (spongiform encephalopathy): transmission to the chimpanzee. Science 1968; 161: 388-9.
-
(1968)
Science
, vol.161
, pp. 388-389
-
-
Gibbs Jr, C.J.1
Gajdusek, D.C.2
Asher, D.M.3
-
5
-
-
0014080385
-
Cannibalism in the kuru region of New Guinea
-
Glasse RM. Cannibalism in the kuru region of New Guinea. Trans N Y Acad Sci 1967; 29: 748-54.
-
(1967)
Trans N Y Acad Sci
, vol.29
, pp. 748-754
-
-
Glasse, R.M.1
-
6
-
-
33745440706
-
st century - an acquired human prion disease with very long incubation periods
-
st century - an acquired human prion disease with very long incubation periods. Lancet 2006; 367: 2068-74.
-
(2006)
Lancet
, vol.367
, pp. 2068-2074
-
-
Collinge, J.1
Whitfield, J.2
McKintosh, E.3
-
7
-
-
65349173916
-
Lack of evidence of transfusion transmission of Creutzfeldt-Jakob disease in a US surveillance study
-
Dorsey KA, Zou S, Schonberger LB et al. Lack of evidence of transfusion transmission of Creutzfeldt-Jakob disease in a US surveillance study. Transfusion 2009; 49: 977-84.
-
(2009)
Transfusion
, vol.49
, pp. 977-984
-
-
Dorsey, K.A.1
Zou, S.2
Schonberger, L.B.3
-
8
-
-
0021752457
-
Purification and structural studies of a major scrapie prion protein
-
Prusiner SB, Groth DF, Bolton DC, Kent SB, Hood LE. Purification and structural studies of a major scrapie prion protein. Cell 1984; 38: 127-34.
-
(1984)
Cell
, vol.38
, pp. 127-134
-
-
Prusiner, S.B.1
Groth, D.F.2
Bolton, D.C.3
Kent, S.B.4
Hood, L.E.5
-
9
-
-
0002812673
-
Prions
-
In: Frängsmyr T, ed. Stockholm: Almqvist & Wiksell International
-
Prusiner SB. Prions. In: Frängsmyr T, ed. Nobel Lecture. Stockholm: Almqvist & Wiksell International, 1997; 268-323.
-
(1997)
Nobel Lecture
, pp. 268-323
-
-
Prusiner, S.B.1
-
10
-
-
77951969247
-
A cellular gene encodes scrapie PrP 27-30 protein
-
Oesch B, Westaway D, Wälchli M et al. A cellular gene encodes scrapie PrP 27-30 protein. Cell 1986; 46: 417-28.
-
(1986)
Cell
, vol.46
, pp. 417-428
-
-
Oesch, B.1
Westaway, D.2
Wälchli, M.3
-
11
-
-
0026600865
-
Normal development and behaviour of mice lacking the neuronal cell-surface PrP protein
-
Büeler H, Fischer M, Lang Y et al. Normal development and behaviour of mice lacking the neuronal cell-surface PrP protein. Nature 1992; 356: 577-82.
-
(1992)
Nature
, vol.356
, pp. 577-582
-
-
Büeler, H.1
Fischer, M.2
Lang, Y.3
-
12
-
-
0027319326
-
Mice devoid of PrP are resistant to scrapie
-
Büeler H, Aguzzi A, Sailer A et al. Mice devoid of PrP are resistant to scrapie. Cell 1993; 73: 1339-47.
-
(1993)
Cell
, vol.73
, pp. 1339-1347
-
-
Büeler, H.1
Aguzzi, A.2
Sailer, A.3
-
13
-
-
0027491308
-
Ablation of the prion protein (PrP) gene in mice prevents scrapie and facilitates production of anti-PrP antibodies
-
Prusiner SB, Groth D, Serban A et al. Ablation of the prion protein (PrP) gene in mice prevents scrapie and facilitates production of anti-PrP antibodies. Proc Natl Acad Sci USA 1993; 90: 10608-12.
-
(1993)
Proc Natl Acad Sci USA
, vol.90
, pp. 10608-10612
-
-
Prusiner, S.B.1
Groth, D.2
Serban, A.3
-
14
-
-
0033850051
-
Scrapie infectivity is independent of amyloid staining properties of the N-terminally truncated prion protein
-
Wille H, Prusiner SB, Cohen FE. Scrapie infectivity is independent of amyloid staining properties of the N-terminally truncated prion protein. J Struct Biol 2000; 130: 323-38.
-
(2000)
J Struct Biol
, vol.130
, pp. 323-338
-
-
Wille, H.1
Prusiner, S.B.2
Cohen, F.E.3
-
15
-
-
0031456947
-
Structure of the recombinant full-length hamster protein PrP (29-231): the N terminus is highly flexible
-
Donne DG, Viles JH, Groth D et al. Structure of the recombinant full-length hamster protein PrP (29-231): the N terminus is highly flexible. Proc Natl Acad Sci USA 1997; 94: 7279-82.
-
(1997)
Proc Natl Acad Sci USA
, vol.94
, pp. 7279-7282
-
-
Donne, D.G.1
Viles, J.H.2
Groth, D.3
-
16
-
-
0030836511
-
NMR characterization of the full-length recombinant murine prion protein, mPrP (23-231)
-
Riek R, Hornemann S, Wider G, Glockshuber R, Wüthrich K. NMR characterization of the full-length recombinant murine prion protein, mPrP (23-231). FEBS Lett 1997; 413: 282-8.
-
(1997)
FEBS Lett
, vol.413
, pp. 282-288
-
-
Riek, R.1
Hornemann, S.2
Wider, G.3
Glockshuber, R.4
Wüthrich, K.5
-
17
-
-
0030728039
-
Deadly conformations - Protein misfolding in prion disease
-
Horwich AL, Weissman JS. Deadly conformations - Protein misfolding in prion disease. Cell 1997; 89: 499-510.
-
(1997)
Cell
, vol.89
, pp. 499-510
-
-
Horwich, A.L.1
Weissman, J.S.2
-
18
-
-
58149378573
-
Prion diseases are effectively transmitted by blood transfusion in sheep
-
Houston F, McCutcheon S, Goldmnann W et al. Prion diseases are effectively transmitted by blood transfusion in sheep. Blood 2008; 112: 4739-45.
-
(2008)
Blood
, vol.112
, pp. 4739-4745
-
-
Houston, F.1
McCutcheon, S.2
Goldmnann, W.3
-
19
-
-
37149043763
-
Creutzfeldt-Jakob disease: reflections on the risk from blood product therapy
-
Brown P. Creutzfeldt-Jakob disease: reflections on the risk from blood product therapy. Haemophilia 2007; 13: 33-40.
-
(2007)
Haemophilia
, vol.13
, pp. 33-40
-
-
Brown, P.1
-
20
-
-
0016398968
-
Possible person to person transmission of Creutzfeldt-Jakob disease
-
Duffy P, Wolf J, Collins G, DeVoe AG, Steeten B, Cowen D. Possible person to person transmission of Creutzfeldt-Jakob disease. N Engl J Med 1974; 299: 692-3.
-
(1974)
N Engl J Med
, vol.299
, pp. 692-693
-
-
Duffy, P.1
Wolf, J.2
Collins, G.3
DeVoe, A.G.4
Steeten, B.5
Cowen, D.6
-
21
-
-
0020077296
-
Evidence for case-to-case transmission of Creutzfeldt-Jakob disease
-
Will RG, Mathews WB. Evidence for case-to-case transmission of Creutzfeldt-Jakob disease. J Neurol Neurosurg Psychiatry 1982; 45: 235-8.
-
(1982)
J Neurol Neurosurg Psychiatry
, vol.45
, pp. 235-238
-
-
Will, R.G.1
Mathews, W.B.2
-
22
-
-
0342951746
-
A new variant of Creutzfeldt-Jakob disease in the UK
-
Will RG, Ironside JW, Zeidler M et al. A new variant of Creutzfeldt-Jakob disease in the UK. Lancet 1996; 347: 921-5.
-
(1996)
Lancet
, vol.347
, pp. 921-925
-
-
Will, R.G.1
Ironside, J.W.2
Zeidler, M.3
-
23
-
-
79959333840
-
-
The National Creutzfeldt-Jakob Disease Surveillance Unit (NCJDSU), University of Edinburgh, UK, Available at:, Accessed November 30, 2010.
-
The National Creutzfeldt-Jakob Disease Surveillance Unit (NCJDSU), University of Edinburgh, UK, Available at:, Accessed November 30, 2010.
-
-
-
-
24
-
-
72249109696
-
Variant CJD in an individual heterozygous for PRNP codon 129
-
Kaski D, Mead S, Hyare H et al. Variant CJD in an individual heterozygous for PRNP codon 129. Lancet 2009; 374: 2128.
-
(2009)
Lancet
, vol.374
, pp. 2128
-
-
Kaski, D.1
Mead, S.2
Hyare, H.3
-
25
-
-
1142273431
-
Possible transmission of variant Creutzfeldt-Jakob disease by blood transfusion
-
Llewelyn CA, Hewitt RE, Knight RSG et al. Possible transmission of variant Creutzfeldt-Jakob disease by blood transfusion. Lancet 2004; 363: 417-21.
-
(2004)
Lancet
, vol.363
, pp. 417-421
-
-
Llewelyn, C.A.1
Hewitt, R.E.2
Knight, R.S.G.3
-
26
-
-
4043157677
-
Preclinical vCJD after blood transfusion in a PRNP codon 129 heterozygous patient
-
Peden AH, Head MW, Ritchie DL, Bell JE, Ironside JW. Preclinical vCJD after blood transfusion in a PRNP codon 129 heterozygous patient. Lancet 2004; 364: 527-9.
-
(2004)
Lancet
, vol.364
, pp. 527-529
-
-
Peden, A.H.1
Head, M.W.2
Ritchie, D.L.3
Bell, J.E.4
Ironside, J.W.5
-
27
-
-
0020522298
-
Creutzfeldt-Jakob disease in mice: persistent viremia and preferential replication of virus in low-density lymphocytes
-
Kuroda Y, Gibbs CJ Jr, Amyx HL, Gajdusek DC. Creutzfeldt-Jakob disease in mice: persistent viremia and preferential replication of virus in low-density lymphocytes. Infect Immunol 1983; 41: 154-61.
-
(1983)
Infect Immunol
, vol.41
, pp. 154-161
-
-
Kuroda, Y.1
Gibbs Jr, C.J.2
Amyx, H.L.3
Gajdusek, D.C.4
-
28
-
-
4043054277
-
Effectiveness of leucoreduction for removal of infectivity of transmissible spongiform encephalopathies from blood
-
Gregori L, McCombie DP, Palmer D, Sowemimo-Coker AO, Giulivi A, Rohwer RG. Effectiveness of leucoreduction for removal of infectivity of transmissible spongiform encephalopathies from blood. Lancet 2004; 264: 529-31.
-
(2004)
Lancet
, vol.264
, pp. 529-531
-
-
Gregori, L.1
McCombie, D.P.2
Palmer, D.3
Sowemimo-Coker, A.O.4
Giulivi, A.5
Rohwer, R.G.6
-
29
-
-
0014211846
-
Does the agent of scrapie replicate without nucleic acid?
-
Alper T, Cramp WA, Haig DA, Clarke MC. Does the agent of scrapie replicate without nucleic acid? Nature 1967; 214: 764-6.
-
(1967)
Nature
, vol.214
, pp. 764-766
-
-
Alper, T.1
Cramp, W.A.2
Haig, D.A.3
Clarke, M.C.4
-
30
-
-
0014190760
-
Self-replication and scrapie
-
Griffith JS. Self-replication and scrapie. Nature 1967; 215: 1043-4.
-
(1967)
Nature
, vol.215
, pp. 1043-1044
-
-
Griffith, J.S.1
-
31
-
-
40749088877
-
A new liquid intravenous immunoglobulin with three dedicated virus reduction steps: virus and prion reduction capacity
-
Poelser G, Berting A, Kindermann J et al. A new liquid intravenous immunoglobulin with three dedicated virus reduction steps: virus and prion reduction capacity. Vox Sang 2008; 94: 184-92.
-
(2008)
Vox Sang
, vol.94
, pp. 184-192
-
-
Poelser, G.1
Berting, A.2
Kindermann, J.3
-
32
-
-
47349084677
-
Prion safety of transfusion plasma and plasma-derivatives typically used for prophylactic treatment
-
Svae T-E, Neisser-Svae A, Bailey A et al. Prion safety of transfusion plasma and plasma-derivatives typically used for prophylactic treatment. Transf Apheres Sci 2008; 39: 59-67.
-
(2008)
Transf Apheres Sci
, vol.39
, pp. 59-67
-
-
Svae, T.-E.1
Neisser-Svae, A.2
Bailey, A.3
-
33
-
-
33746501354
-
Reduction of transmissible spongiform encephalopathy infectivity from human red blood cells with prion protein affinity ligands
-
Gregori L, Lambert B, Gurgel P et al. Reduction of transmissible spongiform encephalopathy infectivity from human red blood cells with prion protein affinity ligands. Transfusion 2009; 46: 1152-61.
-
(2009)
Transfusion
, vol.46
, pp. 1152-1161
-
-
Gregori, L.1
Lambert, B.2
Gurgel, P.3
-
34
-
-
70349559216
-
Prion removal effect of a specific affinity ligand introduced into the manufacturing process of the pharmaceutical quality solvent/detergent(S/D)-treated plasma OctaplasLG
-
Neisser-Svae A, Bailey A, Gregori L et al. Prion removal effect of a specific affinity ligand introduced into the manufacturing process of the pharmaceutical quality solvent/detergent(S/D)-treated plasma OctaplasLG. Vox Sang 2009; 97: 226-33.
-
(2009)
Vox Sang
, vol.97
, pp. 226-233
-
-
Neisser-Svae, A.1
Bailey, A.2
Gregori, L.3
-
36
-
-
79959346994
-
-
Health Protection Agency. Variant CJD and plasma products
-
Health Protection Agency. Variant CJD and plasma products, 2009.
-
(2009)
-
-
-
37
-
-
0842281643
-
Mammalian prion biology: one century of evolving concepts
-
Aguzzi A, Polymenidou M. Mammalian prion biology: one century of evolving concepts. Cell 2004; 116: 313-27.
-
(2004)
Cell
, vol.116
, pp. 313-327
-
-
Aguzzi, A.1
Polymenidou, M.2
-
38
-
-
70349705441
-
Prions: Protein aggregation and infectious disease
-
Aguzzi A, Calella AM. Prions: Protein aggregation and infectious disease. Physiol Rev 2009; 89: 1105-52.
-
(2009)
Physiol Rev
, vol.89
, pp. 1105-1152
-
-
Aguzzi, A.1
Calella, A.M.2
-
39
-
-
33750310849
-
Prions and their partners in crime
-
Caughey B, Baron GS. Prions and their partners in crime. Nature 2006; 443: 803-10.
-
(2006)
Nature
, vol.443
, pp. 803-810
-
-
Caughey, B.1
Baron, G.S.2
-
40
-
-
51649087972
-
Physiological role of the cellular prion protein (PrP-C): protein profiling study in two cell culture systems
-
Ramijak S, Asif AR, Armstrong VW et al. Physiological role of the cellular prion protein (PrP-C): protein profiling study in two cell culture systems. J Proteome Res 2008; 7: 2681-95.
-
(2008)
J Proteome Res
, vol.7
, pp. 2681-2695
-
-
Ramijak, S.1
Asif, A.R.2
Armstrong, V.W.3
-
41
-
-
42049099020
-
Physiology of the prion protein
-
Linden R, Martins VR, Prado MA, Cammarota M, Izquierdo I, Brentani RR. Physiology of the prion protein. Physiol Rev 2008; 88: 673-728.
-
(2008)
Physiol Rev
, vol.88
, pp. 673-728
-
-
Linden, R.1
Martins, V.R.2
Prado, M.A.3
Cammarota, M.4
Izquierdo, I.5
Brentani, R.R.6
-
42
-
-
79959340884
-
-
Prions. In: Morimoto R, Kelly J, Selkoe D, ed. Additional Perspectives on Protein Homeostasis. Cold Spring Harb Perspect Biol doi:
-
Colby DW, Prusiner SB. Prions. In: Morimoto R, Kelly J, Selkoe D, ed. Additional Perspectives on Protein Homeostasis. Cold Spring Harb Perspect Biol doi:
-
-
-
Colby, D.W.1
Prusiner, S.B.2
-
43
-
-
20344394154
-
Anchorless prion protein results in infectious amyloid disease without clinical scrapie
-
Chesebro B, Trifilo M, Race R et al. Anchorless prion protein results in infectious amyloid disease without clinical scrapie. Science 2005; 104: 1435-9.
-
(2005)
Science
, vol.104
, pp. 1435-1439
-
-
Chesebro, B.1
Trifilo, M.2
Race, R.3
-
44
-
-
61349201380
-
Cellular prion protein mediates impairment of synaptic plasticity by amyloid-beta oligomers
-
Laurén J, Gimbel DA, Nygaard HB, Gilbert JW, Strittmatter Jw. Cellular prion protein mediates impairment of synaptic plasticity by amyloid-beta oligomers. Nature 2009; 457: 1128-33.
-
(2009)
Nature
, vol.457
, pp. 1128-1133
-
-
Laurén, J.1
Gimbel, D.A.2
Nygaard, H.B.3
Gilbert, J.W.4
Strittmatter, J.5
-
45
-
-
77649091387
-
Axonal prion protein is required for peripheral myelin maintenance
-
Bremer J, Baumann F, Tiberi C et al. Axonal prion protein is required for peripheral myelin maintenance. Nat Neurosci 2010; 13: 310-18. doi:.
-
(2010)
Nat Neurosci
, vol.13
, pp. 310-318
-
-
Bremer, J.1
Baumann, F.2
Tiberi, C.3
-
46
-
-
3943084181
-
Emerging principles of conformation-based prion inheritance
-
Chien P, Weissman JS, De Pace AH. Emerging principles of conformation-based prion inheritance. Annu Rev Biochem 2004; 73: 617-56.
-
(2004)
Annu Rev Biochem
, vol.73
, pp. 617-656
-
-
Chien, P.1
Weissman, J.S.2
De Pace, A.H.3
-
47
-
-
33644817188
-
Prion domains: sequences, structures and interactions
-
Ross ED, Minton A, Wickner RB. Prion domains: sequences, structures and interactions. Nat Cell Biol 2005; 7: 1039-44.
-
(2005)
Nat Cell Biol
, vol.7
, pp. 1039-1044
-
-
Ross, E.D.1
Minton, A.2
Wickner, R.B.3
-
48
-
-
63049091236
-
A systematic survey identifies prions and illuminates sequence features of prionogenic proteins
-
Alberti S, Halfmann R, King O, Kapila A, Lindquist S. A systematic survey identifies prions and illuminates sequence features of prionogenic proteins. Cell 2009; 137: 146-58.
-
(2009)
Cell
, vol.137
, pp. 146-158
-
-
Alberti, S.1
Halfmann, R.2
King, O.3
Kapila, A.4
Lindquist, S.5
-
49
-
-
77249122579
-
Prions, protein homeostasis, and phenotypic diversity
-
Halfmann R, Alberti S, Lindquist S. Prions, protein homeostasis, and phenotypic diversity. Trends Cell Biol 2010; 20: 125-34.
-
(2010)
Trends Cell Biol
, vol.20
, pp. 125-134
-
-
Halfmann, R.1
Alberti, S.2
Lindquist, S.3
-
50
-
-
78049361927
-
Epigenetics in the extreme: prions and the inheritance of environmentally acquired traits
-
Halfmann R, Lindquist S. Epigenetics in the extreme: prions and the inheritance of environmentally acquired traits. Science 2010; 330: 629-32.
-
(2010)
Science
, vol.330
, pp. 629-632
-
-
Halfmann, R.1
Lindquist, S.2
-
51
-
-
0015550206
-
Scrapie in mice. Agent-strain differences in the distribution and intensity of grey matter vacuolation
-
Fraser H, Dickinson AG. Scrapie in mice. Agent-strain differences in the distribution and intensity of grey matter vacuolation. J Comp Pathol 1973; 83: 29-40.
-
(1973)
J Comp Pathol
, vol.83
, pp. 29-40
-
-
Fraser, H.1
Dickinson, A.G.2
-
52
-
-
76749109480
-
Darwinian evolution of prions in cell culture
-
Li J, Browning S, Mahal SP, Oelschlegel AM, Weissman C. Darwinian evolution of prions in cell culture. Science 2010; 327: 869-72.
-
(2010)
Science
, vol.327
, pp. 869-872
-
-
Li, J.1
Browning, S.2
Mahal, S.P.3
Oelschlegel, A.M.4
Weissman, C.5
-
53
-
-
77950379326
-
Fatal transmissible amyloid encephalopathy: a new type of prion disease associated with lack of prion membrane anchoring
-
Chesebro B, Race B, Meade-White K et al. Fatal transmissible amyloid encephalopathy: a new type of prion disease associated with lack of prion membrane anchoring. PLoS Pathog 2010; 6: e1000800.
-
(2010)
PLoS Pathog
, vol.6
-
-
Chesebro, B.1
Race, B.2
Meade-White, K.3
-
54
-
-
78951477465
-
Crucial role for prion protein membrane anchoring in the neuroinvasion and neural spread of prion infection
-
PubMed PMID: 21123371.
-
Klingeborn M, Race B, Meade-White KD, Rosenke R, Striebel JF, Chesebro B Crucial role for prion protein membrane anchoring in the neuroinvasion and neural spread of prion infection. J Virol 2011; 85: 1484-94. PubMed PMID: 21123371.
-
(2011)
J Virol
, vol.85
, pp. 1484-1494
-
-
Klingeborn, M.1
Race, B.2
Meade-White, K.D.3
Rosenke, R.4
Striebel, J.F.5
Chesebro, B.6
-
55
-
-
20444440728
-
Structure of the cross-beta spine of amyloid-like fibrils
-
Nelson R, Sawaya MR, Balbirnie M et al. Structure of the cross-beta spine of amyloid-like fibrils. Nature 2005; 435: 773-8.
-
(2005)
Nature
, vol.435
, pp. 773-778
-
-
Nelson, R.1
Sawaya, M.R.2
Balbirnie, M.3
-
56
-
-
34249290108
-
Atomic structures of amyloid cross-beta spines reveal varied steric zippers
-
Sawaya MR, Sambashivan S, Nelson R et al. Atomic structures of amyloid cross-beta spines reveal varied steric zippers. Nature 2007; 447: 453-7.
-
(2007)
Nature
, vol.447
, pp. 453-457
-
-
Sawaya, M.R.1
Sambashivan, S.2
Nelson, R.3
-
57
-
-
69949187643
-
Molecular mechanisms of protein-encoded inheritance
-
Wiltzius JJ, Landau M, Nelson R et al. Molecular mechanisms of protein-encoded inheritance. Nat Struct Mol Biol 2009; 16: 973-8.
-
(2009)
Nat Struct Mol Biol
, vol.16
, pp. 973-978
-
-
Wiltzius, J.J.1
Landau, M.2
Nelson, R.3
-
59
-
-
58549102983
-
De novo generation of a transmissible spongiform encephalopathy by mouse transgenesis
-
Sigurdson CJ, Nilsson KP, Hornemann S et al. De novo generation of a transmissible spongiform encephalopathy by mouse transgenesis. Proc Natl Acad Sci 2009; 106: 304-9.
-
(2009)
Proc Natl Acad Sci
, vol.106
, pp. 304-309
-
-
Sigurdson, C.J.1
Nilsson, K.P.2
Hornemann, S.3
-
60
-
-
0035859102
-
Sensitive detection of pathological prion protein by cyclic amplification of protein misfolding
-
Saborio GP, Permanne B, Soto C. Sensitive detection of pathological prion protein by cyclic amplification of protein misfolding. Nature 2001; 411: 810-3.
-
(2001)
Nature
, vol.411
, pp. 810-813
-
-
Saborio, G.P.1
Permanne, B.2
Soto, C.3
-
61
-
-
17444413067
-
In vitro generation of infectious scrapie prions
-
Castilla J, Saá P, Hetz C, Soto C. In vitro generation of infectious scrapie prions. Cell 2005; 121: 136-44.
-
(2005)
Cell
, vol.121
, pp. 136-144
-
-
Castilla, J.1
Saá, P.2
Hetz, C.3
Soto, C.4
-
63
-
-
67249123069
-
De novo generation of infectious prions in vitro produces a new disease phenotype
-
Barria MA, Mukherjee A, Gonzales-Romero D et al. De novo generation of infectious prions in vitro produces a new disease phenotype. PLoS Pathog 2009; 5: e1000421.
-
(2009)
PLoS Pathog
, vol.5
-
-
Barria, M.A.1
Mukherjee, A.2
Gonzales-Romero, D.3
-
64
-
-
77649213673
-
Generating a prion with a bacterially expressed recombinant prion protein
-
Wang F, Wang X, Yuan CG, Ma J. Generating a prion with a bacterially expressed recombinant prion protein. Science 2010; 327: 1132-5.
-
(2010)
Science
, vol.327
, pp. 1132-1135
-
-
Wang, F.1
Wang, X.2
Yuan, C.G.3
Ma, J.4
-
65
-
-
0031586212
-
Molecular properties of complexes formed between the prion protein and synthetic peptides
-
Kaneko K, Wille H, Mehlhorn I et al. Molecular properties of complexes formed between the prion protein and synthetic peptides. J Mol Biol 1997; 270: 574-86.
-
(1997)
J Mol Biol
, vol.270
, pp. 574-586
-
-
Kaneko, K.1
Wille, H.2
Mehlhorn, I.3
-
67
-
-
34447639732
-
Continuum of prion protein structures enciphers a multitude of prion isolate-specific phenotypes
-
Legname G, Nguyen H-OB, Peretz D et al. Continuum of prion protein structures enciphers a multitude of prion isolate-specific phenotypes. Proc Natl Acad Sci 2006; 103: 19105-10.
-
(2006)
Proc Natl Acad Sci
, vol.103
, pp. 19105-19110
-
-
Legname, G.1
Nguyen, H.-O.2
Peretz, D.3
-
68
-
-
73949160065
-
Design and construction of diverse mammalian prion strains
-
Colby DW, Giles K, Legname G et al. Design and construction of diverse mammalian prion strains. Proc Natl Acad Sci 2009; 106: 20417-22.
-
(2009)
Proc Natl Acad Sci
, vol.106
, pp. 20417-20422
-
-
Colby, D.W.1
Giles, K.2
Legname, G.3
-
70
-
-
77956276348
-
Spontaneous generation of mammalian prions
-
Edgeworth JA, Gros N, Alden J et al. Spontaneous generation of mammalian prions. Proc Natl Acad Sci 2010; 107: 14402-6. DOI:.
-
(2010)
Proc Natl Acad Sci
, vol.107
, pp. 14402-14406
-
-
Edgeworth, J.A.1
Gros, N.2
Alden, J.3
-
72
-
-
67649286622
-
Beyond the prion principle
-
Aguzzi A. Beyond the prion principle. Nature 2009; 459: 924-5.
-
(2009)
Nature
, vol.459
, pp. 924-925
-
-
Aguzzi, A.1
-
73
-
-
33749020837
-
Exogenous induction of cerebral beta-amyloidogenesis is governed by agent and host
-
Meyer-Luehmann M, Coomaraswamy J, Bolmont T et al. Exogenous induction of cerebral beta-amyloidogenesis is governed by agent and host. Science 2006; 313: 1781-4.
-
(2006)
Science
, vol.313
, pp. 1781-1784
-
-
Meyer-Luehmann, M.1
Coomaraswamy, J.2
Bolmont, T.3
-
74
-
-
69149098707
-
Indiction of cerebral beta-amyloidosis: intracerebral versus systemic A-beta inoculation
-
Eisele YS, Bolmont T, Heikenwalder M et al. Indiction of cerebral beta-amyloidosis: intracerebral versus systemic A-beta inoculation. Proc Natl Acad Sci 2009; 106: 12926-31.
-
(2009)
Proc Natl Acad Sci
, vol.106
, pp. 12926-12931
-
-
Eisele, Y.S.1
Bolmont, T.2
Heikenwalder, M.3
-
75
-
-
67650077008
-
Transmission and spreading of tauopathy in transgenic mouse brain
-
Clavaguera F, Bolmont T, Crowther RA et al. Transmission and spreading of tauopathy in transgenic mouse brain. Nat Cell Biol 2009; 11: 909-13.
-
(2009)
Nat Cell Biol
, vol.11
, pp. 909-913
-
-
Clavaguera, F.1
Bolmont, T.2
Crowther, R.A.3
-
76
-
-
59649095699
-
Cytoplasmic penetration and persistent infection of mammalian cells by polyglutamine aggregates
-
Ren PH, Lauckner JE, Kachirskaia I, Heuser JE, Melki R, Kopito RR. Cytoplasmic penetration and persistent infection of mammalian cells by polyglutamine aggregates. Nat Cell Biol 2009; 11: 209-25.
-
(2009)
Nat Cell Biol
, vol.11
, pp. 209-225
-
-
Ren, P.H.1
Lauckner, J.E.2
Kachirskaia, I.3
Heuser, J.E.4
Melki, R.5
Kopito, R.R.6
-
77
-
-
17844367336
-
Protein fibrils in nature can enhance amyloid protein a amyloidosis in mice: cross-seeding as a disease mechanism
-
Lundmark K, Westermark GT, Olsen A, Westermark P. Protein fibrils in nature can enhance amyloid protein a amyloidosis in mice: cross-seeding as a disease mechanism. Proc Natl Acad Sci USA 2005; 102: 6098-102.
-
(2005)
Proc Natl Acad Sci USA
, vol.102
, pp. 6098-6102
-
-
Lundmark, K.1
Westermark, G.T.2
Olsen, A.3
Westermark, P.4
-
78
-
-
69149088365
-
Is Parkinson's disease a prion disorder?
-
Olanow CW, Prusiner SB. Is Parkinson's disease a prion disorder? Proc Natl Acad Sci 2009; 106: 12571-2.
-
(2009)
Proc Natl Acad Sci
, vol.106
, pp. 12571-12572
-
-
Olanow, C.W.1
Prusiner, S.B.2
-
79
-
-
0034632806
-
Islet amyloid and type 2 diabetes mellitus
-
Höppener JW, Ahren B, Lips CJ. Islet amyloid and type 2 diabetes mellitus. N Engl J Med 2000; 343: 411-9.
-
(2000)
N Engl J Med
, vol.343
, pp. 411-419
-
-
Höppener, J.W.1
Ahren, B.2
Lips, C.J.3
-
80
-
-
75749134925
-
Aplysia CFEB can form prion-like multimers in sensory neurons that contribute to long-tem facilitation
-
Si K, Choi YB, White-Grindley E, Majumdar A, Kandel ER. Aplysia CFEB can form prion-like multimers in sensory neurons that contribute to long-tem facilitation. Cell 2010; 140: 421-35.
-
(2010)
Cell
, vol.140
, pp. 421-435
-
-
Si, K.1
Choi, Y.B.2
White-Grindley, E.3
Majumdar, A.4
Kandel, E.R.5
|