Hypoplastic Left Heart Syndrome

Surgery for Congenital Heart Defects: Third Edition

Volumn , Issue , 2006, Pages 559-571

  Pizarro, Christian ^a   Norwood, William I ^a  

^a NEMOURS ALFRED I DUPONT HOSPITAL FOR CHILDREN   (United States)

Author keywords

Foetal echocardiography and HLHS diagnosis; Hemi Fontan (Stage two); Hypoplastic left heart syndrome (HLHS); Modified Fontan procedure; Norwood procedure (Stage one)

Indexed keywords

EID: 79958758190     PISSN: None     EISSN: None     Source Type: Book    
DOI: 10.1002/0470093188.ch41     Document Type: Chapter

References (37)

1. Ashburn DA,McCrindle BW, Tchervenkov CI et al. Outcomes after the Norwood operation in neonates with critical aortic stenosis or aortic valve atresia. J Thorac Cardiovasc Surg 125: 1070-1082.
2. Baffa JM, Chen SL, Guttenberg ME et al. Coronary artery abnormalities and right ventricular histology in hypoplastic left heart syndrome. J Am Coll Cardiol 1992; 20: 350-358.
3. Barber G, Helton JG, Aglira BA et al. The significance of tricuspid regurgitation in hypoplastic left-heart syndrome. Am Heart J 1988; 116: 1563-1567.
4. Bharati S,Nordenberg A, Brock RRet al.Hypoplastic left heart syndrome with dysplastic pulmonary valve with stenosis. Pediatr Cardiol 1984; 5: 127-130.
5. Bulkley BH, D'Amico B, Taylor AL. Extensive myocardial fiber disarray in aortic and pulmonary atresia. Relevance to hypertrophic cardiomyopathy. Circulation 1983; 67: 191-198.
6. Chin AJ, Yeager SB, Sanders SP et al. Accuracy of prospective two-dimensional echocardiographic evaluation of left ventricular outflow tract in complete transposition of the great arteries. Am J Cardiol 1985; 55: 759-764.
7. Day RW, Barton AJ, Pysher TJ et al. Pulmonary vascular resistance of children treated with nitrogen during early infancy. Ann Thorac Surg 1998; 65: 1400-1404.
8. Edwards JE. Congenital malformation of the heart and great vessels. In Pathology of the Heart, Gould S E (ed.). C. C. Thomas: Springfield, IL, 1953.
9. Fyler DC. Report of the New England regional infant cardiac program. Pediatrics 1980; 65 (suppl): 375-461.
10. Gullquist SD, Schmitz ML, Hannon CD. Carbon dioxide in the inspired gas improves early postoperative survival in neonates with congenital heart disease following Stage I palliation (Norwood). Circulation 1992; 86 (suppl): I360.
11. Helton JG, Aglira BA, Chin AJ et al. Analysis of potential anatomic or physiologic determinants of outcome of palliative surgery for hypoplastic left heart syndrome. Circulation 1986; 74: I70-76.
12. Imoto Y, Kado H, Shiokawa Y et al. Norwood procedure without circulatory arrest. Ann Thorac Surg 1999; 68: 559-561.
13. Isaaz K, Cloez JL, Danchin N et al. Assessment of right ventricular outflow tract in children by two-dimensional echocardiography using a new subcostal view. Angiocardiographic and morphologic correlative study. Am J Cardiol 1985; 56: 539-545.
14. Kishimoto H, Kawahira Y, Kawata H et al. The modified Norwood palliation on a beating heart. J Thorac Cardiovasc Surg 1999; 118: 1130-1132.
15. Lehman E. Congenital atresia of the foramen ovate. Am J Dis Child 1927; 33: 585-587.
16. Lev M. Pathologic anatomy and interrelationship of hypoplasia of the aortic tract complexes. Lab Invest 1952; 1: 61-70.
17. Lev M, Arcilla R, Rimoldi HJ et al. Premature narrowing or closure of the foramen ovale. Am Heart J 1963; 65: 638-647.
18. Maher KO, Pizarro C, Gidding SS et al. Hemodynamic profile after the Norwood procedure with right ventricle to pulmonary artery conduit. Circulation 2003; 108: 782-784.
19. Mair R, Tulzer G, Sames E et al.Right ventricular to pulmonary artery conduit instead of modified Blalock-Taussig shunt improves postoperative hemodynamics in newborns after the Norwood operation. J Thorac Cardiovasc Surg 2003; 126: 1378-1384.
20. Marino B, de Simone G, Pasquini L et al. Complete transposition of the great arteries: visualization of left and right outflow tract obstruction by oblique subcostal two-dimensional echocardiography. Am J Cardiol 1985; 55: 1140-1145.
21. Mitchell MB, Campbell DN, Boucek MM et al. Mechanical limitation of pulmonary blood flow facilitates heart transplantation in older infants with hypoplastic left heart syndrome. Eur J Cardiothorac Surg 2003; 23: 735-742.
22. Noonan JA, Nadas AS. The hypoplastic left heart syndrome; an analysis of 101 cases. PediatrClinNAm1958; 5: 1029-1056.
23. Norwood WI, Jacobs ML. Fontan's procedure in two stages. Am J Surg 1993; 166: 548-551.
24. Norwood WI, Lang P, Casteneda A R et al. Experience with operations for hypoplastic left heart syndrome. J Thorac Cardiovasc Surg 1981; 82: 511-519.
25. Pizarro C, Malec E, Maher KO et al. Right ventricle to pulmonary artery conduit improves outcome after stage 1. Norwood for hypoplastic left heart syndrome. Circulation 2003c; 108 (suppl 1): II: 155-160.
26. Pizarro C, Mroczek T, Malec E et al. Right ventricle to pulmonary artery conduit reduces interim mortality after stage 1 Norwood for hypoplastic left heart syndrome. Ann Thorac Surg 2004; 78: 1959-1964; discussion, 1959-1964.
27. Pizarro C, Norwood WI. Pulmonary artery banding before Norwood procedure. Ann Thorac Surg 2003a; 75: 1008-1010.
28. Pizarro C, Norwood WI. Right ventricle to pulmonary artery conduit has a favorable impact on postoperative physiology after Stage I Norwood: preliminary results. Eur J Cardiothorac Surg 2003b; 23: 991-995.
29. Roberts WC, Perry LW, Chandra RS et al. Aortic valve atresia: a new classification based on necropsy study of 73 cases. Am J Cardiol 1976; 37: 753-756.
30. Rychik J, Rome JJ, Collins MH et al. The hypoplastic left heart syndrome with intact atrial septum: atrial morphology, pulmonary vascular histopathology and outcome. J Am Coll Cardiol 1999; 34: 554-560.
31. Sano S, Ishino K, Kawada M et al. Right ventricle-pulmonary artery shunt in first-stage palliation of hypoplastic left heart syndrome. J Thorac Cardiovasc Surg 2003; 126: 504-509; discussion, 509-510.
32. Seliem MA, Chin AJ, Norwood WI. Patterns of anomalous pulmonary venous connection/drainage in hypoplastic left heart syndrome: diagnostic role of Doppler color flow mapping and surgical implications. J Am Coll Cardiol 1992; 19: 135-141.
33. Tweddell JS, Hoffman GM, Fedderly RT et al. Phenoxybenzamine improves systemic oxygen delivery after the Norwood procedure. Ann Thorac Surg 1999; 67: 161-167; discussion, 167-168.
34. Vlahos AP, Lock JE, McElhinney DB et al. Hypoplastic left heart syndrome with intact or highly restrictive atrial septum: outcome after neonatal transcatheter atrial septostomy. Circulation 2004; 109: 2326-2330.
35. Watson DG, Rowe RD.Aortic-valve atresia. Report of 43 cases. J Am Med Assoc 1962; 179: 14-18.
36. Weinberg PM, Chin AJ,Murphy JD et al. Postmortem echocardiography and tomographic anatomy of hypoplastic left heart syndrome after palliative surgery. Am J Cardiol 1986; 58: 1228-1232.
37. Dandolu BR, Jacobs ML. Recent advances in reconstructive surgical management of hypoplastic left heart syndrome. Adv Card Surg 2001; 13: 21-60.