NARP mutation and mtDNA depletion trigger mitochondrial biogenesis which can be modulated by selenite supplementation

International Journal of Biochemistry and Cell Biology

Volumn 43, Issue 8, 2011, Pages 1178-1186

  Wojewoda, Marta ^a   Duszyński, Jerzy ^a   Szczepanowska, Joanna ^a  

^a NENCKI INSTITUTE OF EXPERIMENTAL BIOLOGY   (Poland)

Author keywords

Mitochondrial biogenesis; Mitochondrial disease; Mitochondrial stress; NARP; Selenium

Indexed keywords

CYTOCHROME C; GA BINDING PROTEIN; MITOCHONDRIAL DNA; NARP PROTEIN; NUCLEAR RESPIRATORY FACTOR 1; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR GAMMA COACTIVATOR 1ALPHA; REACTIVE OXYGEN METABOLITE; SELENITE; UNCLASSIFIED DRUG;

ARTICLE; BIOGENESIS; CONTROLLED STUDY; ENZYME PHOSPHORYLATION; GENE MUTATION; HUMAN; HUMAN CELL; MITOCHONDRIAL DNA DEPLETION; UPREGULATION;

CELL LINE, TUMOR; CELLS, CULTURED; CYTOCHROMES C; DIETARY SUPPLEMENTS; DNA, MITOCHONDRIAL; DNA-BINDING PROTEINS; FIBROBLASTS; HEAT-SHOCK PROTEINS; HSP70 HEAT-SHOCK PROTEINS; HUMANS; IMMUNOHISTOCHEMISTRY; ION CHANNELS; MITOCHONDRIA; MITOCHONDRIAL MYOPATHIES; MITOCHONDRIAL PROTEINS; MUTATION; PHOSPHORYLATION; RETINITIS PIGMENTOSA; SODIUM SELENITE; TRANSCRIPTION FACTORS;

EID: 79958704151     PISSN: 13572725     EISSN: 18785875     Source Type: Journal    
DOI: 10.1016/j.biocel.2011.04.011     Document Type: Article

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