Experimental evidence that phenylalanine is strongly associated to oxidative stress in adolescents and adults with phenylketonuria

Molecular Genetics and Metabolism

Volumn 103, Issue 3, 2011, Pages 220-225

  Sanayama, Yoshitami ^a   Nagasaka, Hironori ^a   Takayanagi, Masaki ^a   Ohura, Toshihiro ^b   Sakamoto, Osamu ^b   Ito, Tetsuya ^c   Ishige Wada, Mika ^d   Usui, Hiromi ^d   Yoshino, Makoto ^e   Ohtake, Akira ^f   Yorifuji, Tohru ^g   Tsukahara, Hirokazu ^h   Hirayama, Satoshi ⁱ   Miida, Takashi ⁱ   Fukui, Mitsuru ^j   Okano, Yoshiyuki ^j  

^a CHIBA CHILDREN'S HOSPITAL   (Japan)

^b TOHOKU UNIVERSITY HOSPITAL   (Japan)

^c NAGOYA CITY UNIVERSITY GRADUATE SCHOOL OF MEDICAL SCIENCES   (Japan)

^d NIHON UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^e KURUME UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^f SAITAMA MEDICAL UNIVERSITY   (Japan)

^g OSAKA CITY GENERAL HOSPITAL   (Japan)

^h OKAYAMA UNIVERSITY   (Japan)

ⁱ JUNTENDO UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^j OSAKA CITY UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

more..

Author keywords

Diet therapy; Oxidative stress; Phenylalanine; Phenylketonuria

Indexed keywords

3,4 METHYLENEDIOXYAMPHETAMINE; ACROLEIN; ALPHA TOCOPHEROL; ARGININE; BETA CAROTENE; CATALASE; CITRULLINE; GLUTATHIONE PEROXIDASE; LOW DENSITY LIPOPROTEIN; LYSINE; MALONALDEHYDE; N(G),N(G) DIMETHYLARGININE; NITRATE; NITRIC OXIDE; NITRITE; PHENYLALANINE; SUPEROXIDE DISMUTASE; THIOBARBITURIC ACID REACTIVE SUBSTANCE; UBIDECARENONE;

ADOLESCENT; ADULT; AMINO ACID BLOOD LEVEL; ARTICLE; CLINICAL ARTICLE; CONTROLLED STUDY; ENZYME ACTIVITY; ENZYME BLOOD LEVEL; ERYTHROCYTE; FEMALE; HUMAN; LIPOPROTEIN BLOOD LEVEL; MALE; OXIDATIVE STRESS; PHENYLKETONURIA; PRIORITY JOURNAL; VITAMIN BLOOD LEVEL;

ADOLESCENT; ADULT; BIOLOGICAL MARKERS; ERYTHROCYTES; FEMALE; HUMANS; MALE; MIDDLE AGED; NITRIC OXIDE; OXIDATIVE STRESS; PHENYLALANINE; PHENYLKETONURIAS; YOUNG ADULT;

EID: 79958048557     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2011.03.019     Document Type: Article

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