Current status of understanding the pathogenesis and management of patients with NOMID/CINCA

Current Rheumatology Reports

Volumn 13, Issue 2, 2011, Pages 123-131

  Goldbach Mansky, Raphaela ^a  

^a NATIONAL INSTITUTE OF ARTHRITIS AND MUSCULOSKELETAL AND SKIN DISEASES   (United States)

Author keywords

Anakinra; Autoinflammatory diseases; CAPS; CIAS1; CINCA; Genetic disease; IL 1; IL 1Ra; Neonatal disorder; NLRP3; NOMID

Indexed keywords

CANAKINUMAB; ETANERCEPT; INTERLEUKIN 1; INTERLEUKIN 1BETA; PLACEBO; RECOMBINANT INTERLEUKIN 1 RECEPTOR BLOCKING AGENT; RILONACEPT;

ARTICLE; BLOOD BRAIN BARRIER; BONE DISEASE; CENTRAL NERVOUS SYSTEM DISEASE; CINCA SYNDROME; CLINICAL FEATURE; CYTOKINE PRODUCTION; DISEASE EXACERBATION; DRUG CEREBROSPINAL FLUID LEVEL; DRUG DOSE COMPARISON; DRUG HALF LIFE; DRUG MECHANISM; DRUG PENETRATION; DRUG RESPONSE; DRUG SAFETY; EYE INFLAMMATION; FAMILIAL COLD AUTOINFLAMMATORY SYNDROME; GENE; GENE MUTATION; HEARING LOSS; HUMAN; INFECTION; INJECTION SITE REACTION; LONG TERM CARE; MUCKLE WELLS SYNDROME; MYCOBACTERIOSIS; NLRP3 GENE; NONHUMAN; PATHOGENESIS; PNEUMOCOCCAL MENINGITIS; RISK FACTOR; SKIN DISEASE; VERTIGO;

ADOLESCENT; ANIMALS; ANTIRHEUMATIC AGENTS; CARRIER PROTEINS; CHILD; CRYOPYRIN-ASSOCIATED PERIODIC SYNDROMES; DRUG EVALUATION, PRECLINICAL; HUMANS; INFANT, NEWBORN; INFANT, NEWBORN, DISEASES; INFLAMMASOMES; INTERLEUKIN 1 RECEPTOR ANTAGONIST PROTEIN; INTERLEUKIN-1BETA; MUTATION; SYNDROME;

EID: 79957456776     PISSN: 15233774     EISSN: 15346307     Source Type: Journal    
DOI: 10.1007/s11926-011-0165-y     Document Type: Article

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