A classification of ductal plate malformations based on distinct pathogenic mechanisms of biliary dysmorphogenesis

Hepatology

Volumn 53, Issue 6, 2011, Pages 1959-1966

  Raynaud, Peggy ^a   Tate, Joshua ^c   Callens, Céline ^d   Cordi, Sabine ^a   Vandersmissen, Patrick ^a   Carpentier, Rodolphe ^a   Sempoux, Christine ^e   Devuyst, Olivier ^b   Pierreux, Christophe E ^a   Courtoy, Pierre ^a   Dahan, Karin ^e   Delbecque, Katty ^f   Lepreux, Sébastien ^g   Pontoglio, Marco ^d   Guay Woodford, Lisa M ^c   Lemaigre, Frédéric P ^a  

^a DE DUVE INSTITUTE   (Belgium)

^b UNIVERSITÉ CATHOLIQUE DE LOUVAIN   (Belgium)

^c UNIVERSITY OF ALABAMA AT BIRMINGHAM   (United States)

^d INSTITUT COCHIN   (France)

^e CLINIQUES UNIVERSITAIRES SAINT LUC   (Belgium)

^f UNIVERSITY OF LIÈGE   (Belgium)

^g INSERM   (France)

Author keywords

[No Author keywords available]

Indexed keywords

CYSTIN 1; HEPATOCYTE NUCLEAR FACTOR 1BETA; HEPATOCYTE NUCLEAR FACTOR 6; TRANSCRIPTION FACTOR; UNCLASSIFIED DRUG;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BILE DUCT CYST; BILE DUCT MALFORMATION; CELL DIFFERENTIATION; CELL MATURATION; DISEASE CLASSIFICATION; DUCTAL PLATE MALFORMATION; FETUS; GENE MUTATION; HUMAN; HUMAN TISSUE; KIDNEY POLYCYSTIC DISEASE; LIVER; MOUSE; NONHUMAN; PRIORITY JOURNAL;

ANIMALS; BILE DUCTS, INTRAHEPATIC; BIOLOGICAL MARKERS; CELL DIFFERENTIATION; CONGENITAL ABNORMALITIES; DISEASE MODELS, ANIMAL; HEPATOCYTE NUCLEAR FACTOR 1-BETA; HEPATOCYTE NUCLEAR FACTOR 6; HUMANS; LIVER; MEMBRANE PROTEINS; MICE; MICE, MUTANT STRAINS; MORPHOGENESIS; POLYCYSTIC KIDNEY DISEASES; POLYCYSTIC KIDNEY, AUTOSOMAL RECESSIVE;

EID: 79957437545     PISSN: 02709139     EISSN: 15273350     Source Type: Journal    
DOI: 10.1002/hep.24292     Document Type: Article

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