Thrombotic thrombocytopenic purpura with severe ADAMTS-13 deficiency in a patient with antiphospholipid antibodies and Charcot-Marie-Tooth disease

Internal Medicine

Volumn 50, Issue 5, 2011, Pages 487-493

  Kosaka, Mayu ^a   Takahashi, Naoto ^a   Saitoh, Hirobumi ^a   Masai, Rie ^a   Ito, Mitsugu ^a   Sato, Ryuta ^a   Wakui, Hideki ^a   Sawada, Kenichi ^a  

^a AKITA UNIVERSITY GRADUATE SCHOOL OF MEDICINE   (Japan)

Author keywords

Adamts 13; Antiphospholipid antibodies (aPL); Charcot Marie Tooth disease (CMT) (4 6 keywords); Thrombotic thrombocytopenic purpura (TTP)

Indexed keywords

ACETYLSALICYLIC ACID; FRESH FROZEN PLASMA; IMMUNOGLOBULIN; PHOSPHOLIPID ANTIBODY; PREDNISOLONE; PREDNISONE; THROMBOCYTE CONCENTRATE; VON WILLEBRAND FACTOR CLEAVING PROTEINASE;

ADULT; ANTIBODY DETECTION; ARTICLE; BLEEDING TENDENCY; BRAIN INFARCTION; CASE REPORT; COOMBS NEGATIVE HEMOLYTIC ANEMIA; DISEASE ASSOCIATION; DISEASE SEVERITY; DRUG MEGADOSE; ENZYME DEFICIENCY; EPISTAXIS; FEMALE; GAIT DISORDER; HEMOLYTIC ANEMIA; HEREDITARY MOTOR SENSORY NEUROPATHY; HUMAN; IDIOPATHIC THROMBOCYTOPENIC PURPURA; IMAGE ANALYSIS; INTELLIGENCE QUOTIENT; LABORATORY TEST; LOW DRUG DOSE; MENTAL DEFICIENCY; MUSCLE ATROPHY; NEUROLOGIC EXAMINATION; NUCLEAR MAGNETIC RESONANCE IMAGING; PHYSICAL EXAMINATION; PLASMA TRANSFUSION; PRIMARY MOTOR CORTEX; PSYCHOMOTOR DISORDER; THROMBOCYTE TRANSFUSION; THROMBOCYTOPENIA; THROMBOTIC THROMBOCYTOPENIC PURPURA; VON WILLEBRAND FACTOR CLEAVING PROTEINASE DEFICIENCY;

ADAM PROTEINS; ADULT; ANTIBODIES, ANTICARDIOLIPIN; ANTIPHOSPHOLIPID SYNDROME; CHARCOT-MARIE-TOOTH DISEASE; FEMALE; HUMANS; PLASMA; PLATELET TRANSFUSION; PREDNISOLONE; PURPURA, THROMBOTIC THROMBOCYTOPENIC;

EID: 79952351453     PISSN: 09182918     EISSN: 13497235     Source Type: Journal    
DOI: 10.2169/internalmedicine.50.4300     Document Type: Article

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