Clinical features of severe acquired ADAMTS13 deficiency in thrombotic thrombocytopenic purpura: The Korean TTP registry experience

International Journal of Hematology

Volumn 93, Issue 2, 2011, Pages 163-169

  Jang, Moon Ju ^a   Chong, So Young ^a   Kim, In Ho ^b   Kim, Jee Hyun ^b   Jung, Chul Won ^c   Kim, Ja Young ^d   Park, Ji Chan ^d   Lee, Sun Min ^e   Kim, Yeo Kyeoung ^f   Lee, Ji Eun ^g   Jang, Sung Su ^h   Kim, Jin Seok ⁱ   Jo, Deog Yeon ^j   Zang, Dae Young ^k   Lee, Young Yiul ^l   Yhim, Ho Young ^m   Oh, Doyeun ^a  

^a CHA University   (South Korea)

^b Seoul National University   (South Korea)

^c Sungkyunkwan University   (South Korea)

^d The Catholic University of Korea   (South Korea)

^e Pusan National University School of Medicine   (South Korea)

^f Chonnam National University Medical School   (South Korea)

^g Korea University College of Medicine   (South Korea)

^h University of Ulsan College of Medicine   (South Korea)

ⁱ Yonsei University College of Medicine   (South Korea)

^j Chungnam National University   (South Korea)

^k Hallym University   (South Korea)

^l Hanyang University   (South Korea)

^m Chonbuk National University Medical School and Hospital   (South Korea)

more..

Author keywords

ADAMTS 13; Microangiopathic hemolytic anemia; Plasma exchange (PE); Thrombotic thrombocytopenic purpura (TTP); Von Willebrand factor (VWF) cleaving protease

Indexed keywords

BILIRUBIN; CREATININE; HEMOGLOBIN; IMMUNOSUPPRESSIVE AGENT; LACTATE DEHYDROGENASE; VON WILLEBRAND FACTOR CLEAVING PROTEINASE;

ADULT; ARTICLE; BLEEDING; CLINICAL FEATURE; CONTROLLED STUDY; CREATININE BLOOD LEVEL; DISEASE SEVERITY; FEMALE; FEVER; HUMAN; KOREA; LACTATE DEHYDROGENASE BLOOD LEVEL; LEUKOCYTE COUNT; MAJOR CLINICAL STUDY; MALE; MORTALITY; NEUROLOGIC DISEASE; PLASMAPHERESIS; PROGNOSIS; RELAPSE; REMISSION; RISK FACTOR; THROMBOCYTE COUNT; THROMBOTIC THROMBOCYTOPENIC PURPURA; TREATMENT RESPONSE;

ADAM PROTEINS; HUMANS; PURPURA, THROMBOTIC THROMBOCYTOPENIC; REGISTRIES; REPUBLIC OF KOREA; RETROSPECTIVE STUDIES;

EID: 79952249613     PISSN: 09255710     EISSN: None     Source Type: Journal    
DOI: 10.1007/s12185-011-0771-5     Document Type: Article

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