Aortic abnormalities in males with Alport syndrome

Nephrology Dialysis Transplantation

Volumn 25, Issue 11, 2010, Pages 3554-3560

  Kashtan, Clifford E ^a   Segal, Yoav ^b   Flinter, Frances ^c   Makanjuola, David ^d   Gan, Jay Sen ^e   Watnick, Terry ^f  

^a UNIVERSITY OF MINNESOTA MEDICAL SCHOOL   (United States)

^b UNIVERSITY OF MINNESOTA   (United States)

^c GUY'S AND ST THOMAS' NHS FOUNDATION TRUST   (United Kingdom)

^d ST HELIER HOSPITAL   (United Kingdom)

^e ROYAL HOBART HOSPITAL   (Australia)

^f JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

Alport syndrome; Aortic aneurysm; Aortic dissection; Type IV collagen

Indexed keywords

COLLAGEN TYPE 4; COLLAGEN TYPE 4 ALPHA5 CHAIN; UNCLASSIFIED DRUG; COL4A5 PROTEIN, HUMAN;

ADOLESCENT; ADULT; ALPORT SYNDROME; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; AORTA ANEURYSM; AORTA DILATATION; AORTA DISEASE; AORTA DISSECTION; AORTA GRAFT; AORTA MEDIA; AORTA VALVE REGURGITATION; AORTA VALVE REPLACEMENT; ARTICLE; BASEMENT MEMBRANE; BICUSPID AORTIC VALVE; CLINICAL ARTICLE; COL4A5 GENE; CONTROLLED STUDY; DIALYSIS; GENE; GENE EXPRESSION; GLOMERULONEPHRITIS; HEMODIALYSIS; HUMAN; HUMAN TISSUE; IMMUNOHISTOCHEMISTRY; KIDNEY BIOPSY; KIDNEY TRANSPLANTATION; MALE; MOUSE; NONHUMAN; PRIORITY JOURNAL; SEX CHROMOSOMAL INHERITANCE; SKIN BIOPSY; THORACIC AORTA; ANIMAL; AORTA; BIOPSY; CASE REPORT; CONGENITAL MALFORMATION; DISSECTING ANEURYSM; GENETICS; MARFAN SYNDROME; MUTATION; NEPHRITIS; PATHOLOGY; SKIN; THORACIC AORTA ANEURYSM;

ADULT; ANEURYSM, DISSECTING; ANIMALS; AORTA; AORTIC ANEURYSM, THORACIC; BIOPSY; COLLAGEN TYPE IV; HUMANS; MALE; MARFAN SYNDROME; MICE; MUTATION; NEPHRITIS, HEREDITARY; SKIN;

EID: 79952200516     PISSN: 09310509     EISSN: 14602385     Source Type: Journal    
DOI: 10.1093/ndt/gfq271     Document Type: Article

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