Congenital Factor VII Deficiency

Textbook of Hemophilia: Second Edition

Volumn , Issue , 2010, Pages 341-347

  Mariani, Guglielmo ^a   Dolce, Alberto ^b  

^a UNIVERSITY OF L'AQUILA   (Italy)

^b UNIVERSITY OF PALERMO   (Italy)

Author keywords

Bleeding free survival analysis in FVII deficiency by gender (IRF7 database); Congenital factor VII deficiency; Factor VII FVII; previous synonyms proconvertin, stable factor, serum prothrombin conversion accelerator (SPCA) ; FVII deficiency diagnosis discordance between prolonged prothrombin time (PT) and aPTT; FVII, rare protein with very short half life especially in children; Mutational spectrum in FVII deficiency from IRF7 database; Plasma levels of FVII and FVIIa in population affected by F7 gene polymorphisms; Recombinant FVIIa first line product for replacement therapy in FVII deficiency; Symptom distribution in FVII deficient females

Indexed keywords

EID: 79951784906     PISSN: None     EISSN: None     Source Type: Book    
DOI: 10.1002/9781444318555.ch51     Document Type: Chapter

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