A human pathology-related mutation prevents import of an aminoacyl-tRNA synthetase into mitochondria

Biochemical Journal

Volumn 433, Issue 3, 2011, Pages 441-446

  Messmer, Marie ^a   Florentz, Catherine ^a   Schwenzer, Hagen ^a   Scheper, Gert C ^b   Van Der Knaap, Marjo S ^b   Maréchal Drouard, Laurence ^a   Sissler, Marie ^a  

^a UNIVERSITÉ DE STRASBOURG   (France)

^b VU UNIVERSITY MEDICAL CENTER   (Netherlands)

Author keywords

Aminoacyl tRNA synthetase; Organelle; Pathology related mutation; Protein import; Translation machinery; Translocation

Indexed keywords

AMINOACYL TRANSFER RNA; SYNTHETASE;

ARTICLE; EMBRYO; GENE MUTATION; HUMAN; HUMAN CELL; IN VITRO STUDY; IN VIVO STUDY; LEUKOENCEPHALOPATHY; MITOCHONDRIAL MEMBRANE; PRIORITY JOURNAL; SIGNAL TRANSDUCTION;

EID: 78751529272     PISSN: 02646021     EISSN: 14708728     Source Type: Journal    
DOI: 10.1042/BJ20101902     Document Type: Article

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