Niemann - pick disease associated with hemophagocytic syndrome;Hemofagositik sendrom ve niemann-pick hastalıg̈ı birliktelig̈i

Turkish Journal of Hematology

Volumn 27, Issue 4, 2010, Pages 303-307

  Karaman, Serap ^a   Urganci, Nafiye ^a   Kutluk, Günsel ^a   Çetinkaya, Feyzullah ^a  

^a SISLI ETFAL TRAINING AND RESEARCH HOSPITAL   (Turkey)

Author keywords

Hemophagocytic lymphohistiocytosis; Hemophagocytic syndrome; Hemophagocytosis; Hemophagocytosis by niemann pick cell; HLH; Niemann pick disease

Indexed keywords

FRESH FROZEN PLASMA; IMMUNOGLOBULIN; SPHINGOMYELIN PHOSPHODIESTERASE;

ARTICLE; BONE MARROW BIOPSY; CASE REPORT; CYTOPENIA; ENZYME ACTIVITY; ERYTHROPHAGOCYTOSIS; FEMALE; FEVER; FOAM CELL; GENE MUTATION; HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS; HUMAN; HUMAN CELL; HUMAN TISSUE; HYPERFERRITINEMIA; HYPERTRIGLYCERIDEMIA; HYPOFIBRINOGENEMIA; INFANT; LABORATORY TEST; LIPID STORAGE; MACROPHAGE; NIEMANN PICK DISEASE; PARENT; PHYSICAL EXAMINATION; SPLEEN; THORAX RADIOGRAPHY; THROMBOCYTE;

EID: 78651382834     PISSN: 13007777     EISSN: 13085263     Source Type: Journal    
DOI: 10.5152/tjh.2010.54     Document Type: Article

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