Different early ER-stress responses in the CLN8mnd mouse model of neuronal ceroid lipofuscinosis

Neuroscience Letters

Volumn 488, Issue 3, 2011, Pages 258-262

  Galizzi, Giacoma ^a   Russo, Domenica ^a   Deidda, Irene ^a   Cascio, Caterina ^a   Passantino, Rosa ^a   Guarneri, Rosetta ^a   Bigini, Paolo ^b   Mennini, Tiziana ^c   Drago, Gaspare ^a   Guarneri, Patrizia ^a  

^a CNR   (Italy)

^b MARIO NEGRI INSTITUTE FOR PHARMACOLOGICAL RESEARCH   (Italy)

^c NONE

Author keywords

Brain; CLN8mnd mouse; ER stress; Inflammation; Retina; Spinal cord

Indexed keywords

ACTIVATING TRANSCRIPTION FACTOR 6; CASPASE 12; CASPASE 3; GLUCOSE REGULATED PROTEIN 78; IMMUNOGLOBULIN ENHANCER BINDING PROTEIN; MITOGEN ACTIVATED PROTEIN KINASE; TUMOR NECROSIS FACTOR ALPHA; TUMOR NECROSIS FACTOR RECEPTOR ASSOCIATED FACTOR 2;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; ASYMPTOMATIC DISEASE; BRAIN CORTEX; BRAIN DYSFUNCTION; CEREBELLUM; CONTROLLED STUDY; DISEASE COURSE; ENDOPLASMIC RETICULUM STRESS; HIPPOCAMPUS; MOTOR NEURON DISEASE; MOUSE; NERVE CELL DEGENERATION; NEURONAL CEROID LIPOFUSCINOSIS; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; RECEPTOR UPREGULATION; RETINA DEGENERATION; SIGNAL TRANSDUCTION; SPINAL CORD;

ANIMALS; BLOTTING, WESTERN; CENTRAL NERVOUS SYSTEM; DISEASE MODELS, ANIMAL; ENDOPLASMIC RETICULUM; GENE EXPRESSION PROFILING; IMMUNOHISTOCHEMISTRY; INFLAMMATION; MEMBRANE PROTEINS; MICE; MICE, INBRED C57BL; NEURONAL CEROID-LIPOFUSCINOSES; SIGNAL TRANSDUCTION; STRESS, PHYSIOLOGICAL;

EID: 78650817466     PISSN: 03043940     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.neulet.2010.11.041     Document Type: Article

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