Living-donor liver transplantation for carbamoyl phosphate synthetase 1 deficiency

Pediatric Transplantation

Volumn 14, Issue 8, 2010, Pages 1036-1040

  Kasahara, Mureo ^a   Sakamoto, Seisuke ^a   Shigeta, Takanobu ^a   Fukuda, Akinari ^a   Kosaki, Rika ^a   Nakazawa, Atsuko ^a   Uemoto, Shinji ^b   Noda, Masahiro ^a   Naiki, Yasuhiro ^a   Horikawa, Reiko ^a  

^a NATIONAL CENTER FOR CHILD HEALTH AND DEVELOPMENT   (Japan)

^b KYOTO UNIVERSITY   (Japan)

Author keywords

carbamoyl phosphate synthetase 1 deficiency; liver transplantation; living donor liver transplantation; metabolic liver disease

Indexed keywords

4 PHENYLBUTYRIC ACID; ARGININE; BENZOIC ACID; CARNITINE; PHENOBARBITAL; STEROID; TACROLIMUS;

ACUTE GRAFT REJECTION; ARTICLE; BILE DUCT OBSTRUCTION; CARBAMOYL PHOSPHATE SYNTHETASE I DEFICIENCY; CHILD; CLINICAL ARTICLE; CONTINUOUS HEMODIAFILTRATION; DIET SUPPLEMENTATION; DRUG BLOOD LEVEL; EPILEPSY; FEEDING; FEMALE; GRAFT SURVIVAL; HETEROZYGOSITY; HISTOPATHOLOGY; HUMAN; HYPERAMMONEMIA; IMMUNOSUPPRESSIVE TREATMENT; INFANT; LIVER DISEASE; LIVER GRAFT REJECTION; LIVER TRANSPLANTATION; LIVING DONOR; LIVING DONOR LIVER TRANSPLANTATION; LOW DRUG DOSE; MEDICAL RECORD REVIEW; METABOLIC DISORDER; ORGAN DONOR; POSTOPERATIVE HEMORRHAGE; PRESCHOOL CHILD; PROTEIN RESTRICTION; QUALITY OF LIFE; RETROSPECTIVE STUDY; TREATMENT INDICATION; TREATMENT OUTCOME;

CARBAMOYL-PHOSPHATE SYNTHASE I DEFICIENCY DISEASE; CHILD, PRESCHOOL; FEMALE; HUMANS; INFANT; LIVER FUNCTION TESTS; LIVER TRANSPLANTATION; LIVING DONORS; MALE; TREATMENT OUTCOME;

EID: 78649874056     PISSN: 13973142     EISSN: 13993046     Source Type: Journal    
DOI: 10.1111/j.1399-3046.2010.01402.x     Document Type: Article

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