Unilateral adrenalectomy can be an alternative therapy for infantile onset Cushing's syndrome caused by ACTH-independent macronodular adrenal hyperplasia with McCune-Albright syndrome

Endocrine Journal

Volumn 57, Issue 9, 2010, Pages 819-824

  Hamajima, Takashi ^a   Maruwaka, Kaori ^a   Homma, Keiko ^b   Matsuo, Kumihiro ^c   Fujieda, Kenji ^c   Hasegawa, Tomonobu ^d  

^a AICHI CHILDREN'S HEALTH AND MEDICAL CENTER   (Japan)

^b KEIO UNIVERSITY HOSPITAL   (Japan)

^c ASAHIKAWA MEDICAL COLLEGE   (Japan)

^d KEIO UNIVERSITY SCHOOL OF MEDICINE   (Japan)

Author keywords

Acth independent macronodular adrenal hyperplasia (AIMAH); Childhood; Cushing's syndrome; McCune albright syndrome (MAS); Unilateral adrenalectomy

Indexed keywords

6BETA IODOMETHYL 19 NORCHOLEST 5(10) EN 3BETA OL I 131; CORTICOTROPIN; CORTICOTROPIN RELEASING FACTOR; CORTISONE; GLUCOCORTICOID; HYDROCORTISONE;

ABDOMINAL RADIOGRAPHY; ADRENAL CORTEX INSUFFICIENCY; ADRENAL HYPERPLASIA; ADRENAL SCINTISCANNING; ADRENALECTOMY; ALBRIGHT SYNDROME; ANAMNESIS; CASE REPORT; CHILD; CIRCADIAN RHYTHM; COMPUTER ASSISTED TOMOGRAPHY; CUSHING SYNDROME; HORMONE SUBSTITUTION; HUMAN; HYDROCORTISONE URINE LEVEL; MALE; MORNING DOSAGE; NOTE; NUCLEAR MAGNETIC RESONANCE IMAGING; ONSET AGE; POSTOPERATIVE COMPLICATION; PRESCHOOL CHILD; TREATMENT RESPONSE;

ADRENAL GLANDS; ADRENAL HYPERPLASIA, CONGENITAL; ADRENALECTOMY; ADRENOCORTICOTROPIC HORMONE; CIRCADIAN RHYTHM; CORTICOTROPIN-RELEASING HORMONE; CUSHING SYNDROME; FIBROUS DYSPLASIA, POLYOSTOTIC; HUMANS; HYDROCORTISONE; INFANT; MALE;

EID: 77957743225     PISSN: 09188959     EISSN: 13484540     Source Type: Journal    
DOI: 10.1507/endocrj.K10E-003     Document Type: Note

References (13)

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