Ganglioside GM3 levels are altered in a mouse model of hibm: Gm3 as a cellular marker of the disease

PLoS ONE

Volumn 5, Issue 4, 2010, Pages

  Paccalet, Thomas ^a   Coulombe, Zoé ^a   Tremblay, Jacques P ^a  

^a UNIVERSITÉ LAVAL   (Canada)

Author keywords

[No Author keywords available]

Indexed keywords

GANGLIOSIDE GM3; GANGLIOSIDE GM3 SYNTHASE; MESSENGER RNA; METHIONINE; SYNTHETASE; THREONINE; UNCLASSIFIED DRUG; BIOLOGICAL MARKER; EPIMERASE; HAEMATOSIDE SYNTHETASE; MULTIENZYME COMPLEX; N ACYLMANNOSAMINE KINASE; N-ACYLMANNOSAMINE KINASE; PHOSPHOTRANSFERASE; SIALYLTRANSFERASE; UDP ACETYLGLUCOSAMINE 2 EPIMERASE; UDP ACETYLGLUCOSAMINE-2-EPIMERASE; UDP N ACETYLGLUCOSAMINE 2 EPIMERASE N ACETYLMANNOSAMINE KINASE; UDP-N-ACETYLGLUCOSAMINE 2-EPIMERASE - N-ACETYLMANNOSAMINE KINASE;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; DISEASE MARKER; GENE EXPRESSION; GENE MUTATION; HEREDITARY INCLUSION BODY MYOPATHY; LIPOGENESIS; MOUSE; MYOPATHY; NONHUMAN; NUCLEOTIDE SEQUENCE; PATHOPHYSIOLOGY; PROTEINURIA; ANIMAL; BIOSYNTHESIS; CHEMISTRY; DISEASE MODEL; GENETICS; INCLUSION BODY MYOSITIS; METABOLISM; MISSENSE MUTATION; SKELETAL MUSCLE;

MAMMALIA; MUS;

ANIMALS; BIOLOGICAL MARKERS; CARBOHYDRATE EPIMERASES; DISEASE MODELS, ANIMAL; G(M3) GANGLIOSIDE; MICE; MULTIENZYME COMPLEXES; MUSCLE, SKELETAL; MUTATION, MISSENSE; MYOSITIS, INCLUSION BODY; PHOSPHOTRANSFERASES (ALCOHOL GROUP ACCEPTOR); RNA, MESSENGER; SIALYLTRANSFERASES;

EID: 77956322898     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0010055     Document Type: Article

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