Complex I disorders: Causes, mechanisms, and development of treatment strategies at the cellular level

Developmental Disabilities Research Reviews

Volumn 16, Issue 2, 2010, Pages 175-182

  Valsecchi, Federica ^a,b   Koopman, Werner J H ^a   Manjeri, Ganesh R ^a,b   Rodenburg, Richard J ^b   Smeitink, Jan A M ^b   Willems, Peter H G M ^a  

^a RADBOUD UNIVERSITY MEDICAL CENTER   (Netherlands)

^b RADBOUD UNIVERSITY MEDICAL CENTER   (Netherlands)

Author keywords

Antioxidants; Membrane potential; Mitochondrial; Reactive oxygen species

Indexed keywords

CELL NUCLEUS DNA; METHYLPLASTOQUINONYLDECYLTRIPHENIL PHOSPHONIUM; MITOCHONDRIAL DNA; PLASTOQUINONE; PLASTOQUINONYLDECYL RHODAMINE; PLASTOQUINONYLDECYL TRIPHENYLPHOSPHONIUM; REACTIVE OXYGEN METABOLITE; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE (UBIQUINONE); RESVERATROL; SIRTUIN 1; UNCLASSIFIED DRUG;

BASAL GANGLION; BRAIN STEM; CHILDHOOD; COMPLEX 1 DISORDER; DISORDERS OF MITOCHONDRIAL FUNCTIONS; FAILURE TO THRIVE; FIBROBLAST; GENE EXPRESSION; GENE STRUCTURE; HUMAN; INHERITANCE; LACTIC ACIDEMIA; LIVE BIRTH; MITOCHONDRIAL RESPIRATION; MUSCLE HYPOTONIA; OXIDATIVE STRESS; PRIORITY JOURNAL; REVIEW; SEIZURE;

EID: 77956232845     PISSN: 19405510     EISSN: 10982779     Source Type: Journal    
DOI: 10.1002/ddrr.107     Document Type: Review

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