A case of adult atypical haemolytic uraemic syndrome related to anti-factor H autoantibodies successfully treated by plasma exchange, corticosteroids and rituximab

NDT Plus

Volumn 2, Issue 6, 2009, Pages 458-460

  Lionet, Arnaud ^a   Provôt, Franois ^a   Glowacki, Franois ^a   Frémeaux Bacchi, Veronique ^b   Hazzan, Marc ^a  

^a LILLE UNIVERSITY HOSPITAL   (France)

^b HÔPITAL EUROPÉEN GEORGES POMPIDOU   (France)

Author keywords

anti CFH autoantibodies; atypical HUS; plasma exchange; rituximab

Indexed keywords

AUTOANTIBODY; BILIRUBIN; COMPLEMENT COMPONENT C3; COMPLEMENT FACTOR H ANTIBODY; COMPLEMENT FACTOR H RELATED PROTEIN; CORTICOSTEROID; CREATININE; FRESH FROZEN PLASMA; HAPTOGLOBIN; HEMOGLOBIN; IMMUNOGLOBULIN G ANTIBODY; LACTATE DEHYDROGENASE; PROTEIN; RITUXIMAB; UNCLASSIFIED DRUG;

ABDOMINAL PAIN; ACUTE KIDNEY FAILURE; ADULT; ANTIBODY BLOOD LEVEL; ANTIBODY DETECTION; ARTICLE; ASTHENIA; ATYPICAL HAEMOLYTIC URAEMIC SYNDROME; BILIRUBIN BLOOD LEVEL; CASE REPORT; CORTICOSTEROID THERAPY; CREATININE BLOOD LEVEL; DIARRHEA; DRUG DOSE REDUCTION; FOLLOW UP; GENE DELETION; GENETIC ANALYSIS; HEMATURIA; HEMODIALYSIS; HEMOGLOBIN BLOOD LEVEL; HEMOLYTIC UREMIC SYNDROME; HETEROZYGOSITY; HISTOPATHOLOGY; HOMOZYGOSITY; HUMAN; HUMAN TISSUE; KIDNEY BIOPSY; LABORATORY TEST; LACTATE DEHYDROGENASE BLOOD LEVEL; MALE; PLASMAPHERESIS; PRIORITY JOURNAL; PROTEINURIA; RELAPSE; THROMBOCYTOPENIA; THROMBOTIC THROMBOCYTOPENIC PURPURA; TREATMENT OUTCOME; URINALYSIS;

EID: 77955803613     PISSN: 17530784     EISSN: 17530792     Source Type: Journal    
DOI: 10.1093/ndtplus/sfp109     Document Type: Article

References (6)

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